Frequency of cutis laxa‐like clinical features and elastolysis in scleromyxedema: a retrospective clinicopathologic study of 19 patients with scleromyxedema

Santiago, Tania M. Gonzalez; Lehman, Julia S.; Buonaccorsi, J. Noelle; Kalaaji, Amer N.; Wieland, C

doi:10.1111/cup.12657

Cited by 6 publications

(1 citation statement)

References 15 publications

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“…Sweat gland proliferations are found occasionally 41 . The elastic fibres are fragmented and decreased in number, explaining the clinical presentation of redundant skin folds on a sclerodermoid background (‘shar pei sign’) 42 . Figure 1 shows an anonymized example of a scleromyxoedema face.…”

Section: Scleromyxoedemamentioning

confidence: 99%

Consensus statement on the diagnosis and treatment of sclerosing diseases of the skin, Part 2: Scleromyxoedema and scleroedema

Knobler,

Geroldinger‐Simić,

Kreuter

et al. 2024

Acad Dermatol Venereol

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The term ‘sclerosing diseases of the skin’ comprises specific dermatological entities, which have fibrotic changes of the skin in common. These diseases mostly manifest in different clinical subtypes according to cutaneous and extracutaneous involvement and can sometimes be difficult to distinguish from each other. The present consensus provides an update to the 2017 European Dermatology Forum Guidelines, focusing on characteristic clinical and histopathological features, diagnostic scores and the serum autoantibodies most useful for differential diagnosis. In addition, updated strategies for the first‐ and advanced‐line therapy of sclerosing skin diseases are addressed in detail. Part 2 of this consensus provides clinicians with an overview of the diagnosis and treatment of scleromyxoedema and scleroedema (of Buschke).

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Section: Scleromyxoedemamentioning

confidence: 99%