Fox-Fordyce Disease With an Atypical Clinical Presentation

Ballester, I.; López-Ávila, Angel; Ortiz, Silva

doi:10.1016/j.adengl.2012.10.015

Cited by 4 publications

(12 citation statements)

References 8 publications

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“…3,[5][6][7][8][9] Teori lain yaitu akibat tingginya aktivitas unit pilosebasea, faktor hormonal, trauma, infeksi, dan reaksi imunologis. 1,4,[10][11][12][13][14][15] Steatocystoma multiplex (sebocystomatosis, epidermal polycystic disease) dengan gejala berupa kista yang sangat banyak. Gangguan ini dapat diturunkan secara autosomal dominan.…”

Section: Steatosistomaunclassified

“…Daerah sternum umumnya dikenai pada laki-laki (gambar 3). 1,[4][5][6]10,11 Steatosistoma dapat muncul berupa lesi tunggal (steatocystoma simplex) ataupun multipel (steatocystoma multiplex). Onset munculnya kista umumnya pada masa remaja atau dewasa muda.…”

Section: Gejala Klinisunclassified

“…Kista umumnya muncul atau menjadi lebih besar pada masa pubertas. 4,5,6,11 Dengan diameter bervariasi mulai dari beberapa milimeter hingga beberapa sentimeter (0.2~2 cm), tetapi nodul dapat menjadi lebih besar. 11 yang mengalirkan cairan berminyak atau berbentuk krim yang khas jika di lakukan insisi.…”

Section: Gejala Klinisunclassified

“…Epidermis umumnya normal tanpa ada punctum pada bagian tengahnya, namun pada beberapa kasus, punctum dapat muncul dengan gambaran yang tidak begitu jelas, serta lesi berupa komedo juga dapat ditemukan. 2,11 Lesi steatosistoma dapat terjadi supurasi supurasi, menyebabkan pembentukan sinus dan jaringan parut. 1,4 Jika terjadi ruptur spontan dari kista, dapat menyebabkan jaringan parut, yang menyerupai akne konglobata akut.…”

Section: Gejala Klinisunclassified

“…Menurut daerah yang dikenai, penyakit ini dapat dikelompokkan menjadi lokalisata, generalisata, fasial dan akral. 2,10,11 Terdapat laporan kasus steatosistoma pada lokasi yang tidak biasa dari dua wanita yang tidak memiliki hubungan kekeluargaan. Steatosistoma multipleks ditemukan pada usia yang lebih tua dan hanya pada vulva.…”

Section: Gejala Klinisunclassified

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Diagnosis dan Tatalaksana Steatosistoma

Kampar

Lestari²

2018

JKA

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AbstrakSteatosistoma adalah suatu kista intradermal yang umumnya asimtomatik dimana kista tersebut berisi sebum dengan karakteristik khas terdapat kelenjar sebasea pada dinding kista yang dilapisi epitel berlapis gepeng. Steatosistoma dapat muncul sebagai lesi tunggal (steatocystoma simplex) dan dapat juga multipel (steatocystoma multiplex). Diagnosis ditegakkan berdasarkan anamnesis dan pemeriksaan fisik serta pemeriksaan histopatologi (jika diperlukan). Masih belum ada terapi standar untuk steatosistoma, terapi sistemik dengan pemberian retinoid oral, tetrasiklin 1 gr/ hari, atau minosiklin 100-200 mg/ hari. Terapi lokal dengan injeksi glukokortikoid intralesi. Tindakan dengan cryosurgery dan radiofrequency. Terapi bedah dengan simple aspiration, eksisi bedah, insisi bedah, serta terapi dengan laser karbondioksida dan laser Er:Yag. Pasien umumnya memiliki keluhan kosmetik, sehingga deteksi dini dan tatalaksana yang baik sangat diperlukan. AbstractSteatocystoma is an intradermal cyst that commonly asimptomatic and the cyst consist of sebum that charracteristic cebacea gland on the cyst wall with cornified stratum corneum. Steatocystoma can be singular (steatocystoma simplex) and multiple (steatocystoma multiplex). Diagnosis based on anamnesis, physical examination and histophatology examination (if needed). There were still no gold standar teraphy. Sistemic teraphy with oral retinoid, tetracyclin 1g/day or minocyclin 100-200 mg/day. Local teraphy with intralesional glucocorticoid. Cryosurgeru and radiofrequency. Surgery with simple aspiration, exicion, laser CO2 and Er:Yag laser. Patient usually complain about cosmetic disturbance, so early detection and prompt teraphy is neded.

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Section: Steatosistomaunclassified

Section: Gejala Klinisunclassified

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Diagnosis dan Tatalaksana Steatosistoma

Kampar

Lestari²

2018

JKA

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Pathophysiology, clinical findings, and management of Fox‐Fordyce disease: A systematic review

Salloum

Bouferraa

Bazzi

et al. 2021

J of Cosmetic Dermatology

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Background: Fox-Fordyce (FFD), also known as apocrine military, is an uncommon chronic inflammation of the apocrine sweat glands. It is characterized by pruritic, papular eruptions in apocrine-gland-bearing regions. FFD was described a century ago, but the exact pathogenesis of the disease and the management are not well understood. Aims:This paper provides a wide understanding of the pathophysiology, clinical findings, and management of Fox-Fordyce disease. Its aim is to help the physician to diagnose and manage this entity accordingly.Methods: A research was done using PubMed database on 12 April 12, 2020, and in order to retrieve all case reports, case series, cohort studies, randomized, and nonrandomized clinical trials were included describing FFD among patients.Results: A total of 43 articles and 68 patients were included in the study. The majority of patients were young females. The disease was bilateral in 90%, affected the axillae and to a lesser extent the pubic and the periareolar areas and rarely the thoracic area, the abdominal area, and the face. FFD followed a relapsing and remitting course, and an evident improvement in disease course was noted after menopause. Conclusion:The typical FFD patient is a post-pubertal female and pre-menopause, presenting with pruritic papules in apocrine-gland-bearing regions. FFD can be sporadic or occurs in family, and it can be asymptomatic in 1/(3-4) of patients and can be triggered by laser hair removal and hormonal changes. Further randomized clinical trials assessing different treatment of FFD are now warranted.

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Fox-Fordyce disease: report of two cases with perifollicular xanthomatosis on histological image

Vega‐Memije

Pérez-Rojas

Boeta-Ángeles

et al. 2018

An. Bras. Dermatol.

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Fox-Fordyce disease is a relatively infrequent pathology of the apocrine glands that affects almost exclusively young women. The disease is characterized by the presence of pruritic follicular papules mainly in the armpits that respond poorly to treatment and severely affect the patient’s quality of life. We report two cases with clinical diagnosis and histopathological confirmation, presenting perifollicular xanthomatosis on histological examination, recently described as a distinctive, consistent, and specific feature of this disease.

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Fox-Fordyce Disease With an Atypical Clinical Presentation

Cited by 4 publications

References 8 publications

Diagnosis dan Tatalaksana Steatosistoma

Diagnosis dan Tatalaksana Steatosistoma

Pathophysiology, clinical findings, and management of Fox‐Fordyce disease: A systematic review

Fox-Fordyce disease: report of two cases with perifollicular xanthomatosis on histological image

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