Fourth Ventricle Neurenteric Cyst Mimicking Hemangioblastoma

Abstract

This report presents a case of fourth ventricle neurenteric cyst (NE cyst) mimicking hemangioblastoma, which developed in a 50-year-old woman. A tiny enhancing mural portion of the fourth ventricle in MRI suggested that the cyst was hemangioblastoma, but pathological evidence showed that the cyst was in fact NE cyst in the fourth ventricle. In order to make proper decision on to what extent of surgical resection should be done, considering every possibility in differential diagnosis might be helpful. This case reports an unusual pathology in 4th ventricle, considering the patient's age, and demonstrates that a rarer disease may share radiological features of a common disease.

Frontal Neurenteric Cysts Combined with Anterior Skull Base Osteoma and Spontaneous Intracranial Pneumatosis：A Case Report and Literature Review

“…The rst report of of neurenteric cysts of CNS was published by Kuba and Fulton in 1928 and were rst described in detail in the spinal region by Puusepp in 1934,the embryopathogenesis of neurenteric cysts is still unclear and various hypotheses have been proposed [1] . The most common hypothesis is that neurenteric cysts arise from failure of dissolution of the neurenteric canal.Intracranial locations occur predominantly anterior to the brainstem, at the cerebellopontine angle and to a lesser extent within the fourth ventricle.Clinical symptoms are due to mass effect, and presentation is therefore variable and related to lesion size and location,the most common clinical manifestations are headache, vertigo, nausea, vomiting, and various cranial nerve de cits depending on lesion location [2,3] .…”