Formation of pannus on prosthetic valves in a child with pseudoxanthoma elasticum

Radford, Dorothy J.; Pohlner, Peter

doi:10.1017/s1047951102000380

Cited by 7 publications

(3 citation statements)

References 9 publications

(9 reference statements)

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“…However, redo replacement for reasons other than PPM should be avoided when possible. The main reason for early redo replacement before PPM is excessive pannus formation, which is much more likely in small children than in adults [16,17]. However, excessive pannus formation did not occur in our cohort.…”

Section: Commentmentioning

confidence: 52%

Clinical Outcomes of Mitral Valve Replacement With the 16-mm ATS Advanced Performance Valve in Neonates and Infants

Moon

Hoashi

Kagisaki

et al. 2015

The Annals of Thoracic Surgery

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Section: Commentmentioning

confidence: 52%

Clinical Outcomes of Mitral Valve Replacement With the 16-mm ATS Advanced Performance Valve in Neonates and Infants

Moon

Hoashi

Kagisaki

et al. 2015

The Annals of Thoracic Surgery

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“…Cases of renovascular hypertension have also been reported 19–21 . Valvular changes, mainly mitral valve prolapse, may be present 22 . Early PXE‐related coronary artery disease is often severe, most cases presenting as early angina pectoris or myocardial infarction, treated by aortocoronary bypass 23–27 .…”

Section: Discussionmentioning

confidence: 99%

“…[19][20][21] Valvular changes, mainly mitral valve prolapse, may be present. 22 Early PXE-related coronary artery disease is often severe, most cases presenting as early angina pectoris or myocardial infarction, treated by aortocoronary bypass. [23][24][25][26][27] In some cases coronary artery disease has led to sudden death.…”

Section: Discussionmentioning

confidence: 99%

Manifestations of pseudoxanthoma elasticum in childhood

Naouri

Boisseau

Bonicel

et al. 2009

British Journal of Dermatology

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Background Pseudoxanthoma elasticum (PXE) affects the skin, retina and cardiovascular system. Most cases are related to mutations in the ABCC6 gene. The diagnosis is most often made late in the second or third decade of life. Objectives To describe the manifestations of PXE before the age of 15 years. Methods Children under age 15 years with definite PXE were evaluated at a PXE referral centre, as were adult patients in whom serious manifestations of PXE had occurred before the age of 15 years. Results Our series included 96 patients; 15 (16%) had paediatric onset of the disease. Nine children were diagnosed at a mean age of 10 years, a mean of 2AE5 years after the presenting symptoms. Cutaneous lesions were the presenting symptoms in eight. None had cardiovascular or ophthalmological symptoms. Six adult patients had had severe cutaneous and/or cardiovascular manifestations before the age of 15 years. Both adult patients with early extensive skin lesions had the PXE-like condition related to the GGCX gene. No ocular symptoms were recorded during childhood. Conclusions Cutaneous manifestations of PXE are the same in children as in young adults. Absence of complications is common in childhood, but severe complications are unpredictable. The frequency of complications was retrospectively estimated to be 7% in the adults of our series, although this figure was probably an overestimate because of the recruitment bias in a referral centre. It is, however, important to consider PXE in the paediatric setting, as early diagnosis may be important to provide accurate information and discuss lifestyle adjustments in order to improve the prognosis of the disease.

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Dysfunction of an ATS valve in the aortic position: the first reported case caused by pannus formation

et al. 2005

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A 64-year-old woman underwent aortic valve replacement with a 21-mm Advancing The Standard (ATS) open-pivot mechanical heart valve for bicuspid aortic valve stenosis. In addition to the appearance of a new cardiac murmur, echocardiography performed 3 years after surgery showed a high pressure gradient across the ATS valve and a reduction in the valve orifice area. Cineradiography of the valve revealed restricted leaflet opening. Subsequent multidetector-row computed tomography clearly demonstrated pannus overgrowth on the inflow aspect of the ATS valve. During a repeat operation, subvalvular overgrown pannus was confirmed and the ATS valve was replaced with a bioprosthetic valve. This is the first reported case of prosthetic valve dysfunction resulting from pannus formation in a patient with an ATS valve in the aortic position.

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Formation of pannus on prosthetic valves in a child with pseudoxanthoma elasticum

Cited by 7 publications

References 9 publications

Clinical Outcomes of Mitral Valve Replacement With the 16-mm ATS Advanced Performance Valve in Neonates and Infants

Clinical Outcomes of Mitral Valve Replacement With the 16-mm ATS Advanced Performance Valve in Neonates and Infants

Manifestations of pseudoxanthoma elasticum in childhood

Dysfunction of an ATS valve in the aortic position: the first reported case caused by pannus formation

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