First Branchial Cleft Anomaly With an Orifice in the Bony External Auditory Canal Accompanied by Contralateral Middle Ear Cholesteatoma

Ohki, Masafumi; Baba, Yuka; Ohata, Atsushi

doi:10.1097/mao.0000000000000411

Cited by 2 publications

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“…Generally, EAC bony atresia means that the bony atresia plank has occupied the normal structure of the EAC. FBCA accompanied by external ear diseases are rare, and to date, only a few FBCA cases accompanied by congenital EAC stenosis or atresia, and cholesteatoma have been reported[ 4 , 9 - 11 ]. Banakis et al[ 4 ] reported a case of bilateral ear canal cholesteatomas in the setting of underlying FBCA.…”

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confidence: 99%

First branchial cleft cyst accompanied by external auditory canal atresia and middle ear malformation: A case report

Zhang¹,

Li²,

Chen³

et al. 2020

WJCC

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BACKGROUND We report a rare case of first branchial cleft anomaly (FBCA) accompanied by bony atresia of the external auditory canal, middle ear malformation, and location malformation of the facial nerve according to the intraoperative findings. CASE SUMMARY A 19-year-old male patient presented to our department with a mass behind the right earlobe and recurrent postauricular swelling and pain since childhood, he also had severe hearing loss in the right ear since birth. The patient underwent surgery including mass removal, mastoidectomy, and simultaneous meatoplasty and ossiculoplasty under microscopy. No facial palsy or recurrence was noted during postoperative follow-up. CONCLUSION FBCAs are rare, and to our knowledge, this is the first report of FBCA accompanied by external auditory canal bony atresia, middle ear malformation, and location malformation of the facial nerve. An effective postauricular approach under microscopy facilitated complete lesion removal and simultaneous otologic reconstruction.

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