Fibrous Dysplasia of the Facial Bones

Meiselman, Frederick

doi:10.1016/s1042-3699(20)30965-1

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2023

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“…Dental procedures are safe to perform in patients with FD and do not adversely affect the course of the disease. Orthognathic surgery, in combination with orthodontic therapy, can also be performed in FD patients at skeletal maturity and disease stabilization [ 60 – 62 ].…”

Section: Managementmentioning

confidence: 99%

Current concepts of craniofacial fibrous dysplasia: pathophysiology and treatment

Kim

2023

Arch Craniofac Surg

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Fibrous dysplasia is an uncommon genetic disorder in which bone is replaced by immature bone and fibrous tissue, manifesting as slowgrowing lesions. Sporadic post-zygotic activating mutations in GNAS gene result in dysregulated GαS-protein signaling and elevation of cyclic adenosine monophosphate in affected tissues. This condition has a broad clinical spectrum, ranging from insignificant solitary lesions to severe disease. The craniofacial area is the most common site of fibrous dysplasia, and nine out of 10 patients with fibrous dysplasia affecting the craniofacial bones present before the age of 5. Surgery is the mainstay of treatment, but the technique varies according to the location and severity of the lesion and associated symptoms. The timing and indications of surgery should be carefully chosen with multidisciplinary consultations and a patient-specific approach.

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Section: Managementmentioning

confidence: 99%

Current concepts of craniofacial fibrous dysplasia: pathophysiology and treatment

Kim

2023

Arch Craniofac Surg

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Fibrous Dysplasia of the Facial Bones

Cited by 1 publication

References 3 publications

Current concepts of craniofacial fibrous dysplasia: pathophysiology and treatment

Current concepts of craniofacial fibrous dysplasia: pathophysiology and treatment

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