Fibrosarcoma of the scalp

Abstract

A parieto-occipital scalp tumor, noted in a Nigerian boy during the first month of his life, gradually increased in size, and after two attempts at partial removal there was a rapid increase in its size. When he was 17 years old, it measured 21 X 17 X 16 cm. There was no underlying skull defect. Complete excision of the tumor was achieved, and on histological examination it was found to be a fibrosarcoma. The patient was given a course of radiotherapy following wound healing. He remained well for 5 1/2 months but then had manifestations of small local recurrence and distant metastases that responded only minimally to another course of radiotherapy combined with cancer chemotherapy.

Congenital (infantile) fibrosarcoma of the scalp: a case series and review of literature

“…Congenital infantile fibrosarcoma of the scalp is very rare, and to the best of our knowledge, excluding the cases in our series, only three cases have been previously published [2][3][4] ( Table 1). The examples of pediatric primary scalp fibrosarcoma cited by Muzmadar et al [3] were not true CIFS, as the youngest patient in one series was 17 years old, while age was not specified in other.…”

“…The age of the patients in our series ranged from 12 to 90 days (mean 48 days), and all patients in our series are also male. The size of tumor in previously reported cases ranged from 5 to 21 cm (mean 13.3 cm) [2][3][4]. Tumor size ranged from 6 to 9.5 cm (mean 8 cm) in our cases.…”

“…Another case was an example of a scalp neurofibrosarcoma, which is the old name of malignant peripheral nerve sheath tumor. Interestingly, all the previously reported cases of CIFS were male patients with age ranging from 1 to 6 months at the time of diagnosis [2][3][4]. The age of the patients in our series ranged from 12 to 90 days (mean 48 days), and all patients in our series are also male.…”

“…Tumor size ranged from 6 to 9.5 cm (mean 8 cm) in our cases. Clinically, the mass was initially slowly growing but later rapidly growing in the case reported by Chaudhari et al [2] and Kumar et al [4]. Muzmadar et al [3], however, reported rapid growth from the start.…”

“…Almost half of all infantile fibrosarcoma cases are congenital [1]. CIFS of the scalp is very rare and only three cases have been reported in the literature [2][3][4]. Herein, we report three cases of congenital fibrosarcoma presenting as scalp mass.…”