Fetal Rhabdomyoma of the Right Tonsil with Polyp-Like Appearance

Abstract

Skeletal muscle neoplasms, in contrast to other groups of tumors, are almost malignant. The benign variant, rhabdomyoma, is distinctly rare. Rhabdomyomas can be classified generally into two types: cardiac and extracardiac. Extracardiac rhabdomyoma can be further divided into three subtypes: adult, fetal, and genital type. Adult rhabdomyoma is the most common subtype of rhabdomyoma even though it remains relatively rare. Fetal rhabdomyomas are less common than the adult type. In this paper we report a rare case of a fetal rhabdomyoma with polyp-like appearance originating from right tonsil. Punch biopsy and then right tonsillectomy were performed for complete excision. There was no obvious recurrence.

Fetal Type Rhabdomyoma of the Soft Palate in an Adult Patient: Report of One Case and Review of the Literature

“…Clinically, majority patients with fetal rhabdomyoma presented with asymptomatic nodule/mass or painless swelling, with the exception of masses located at vocal cord, which often caused hoarseness, and the one tumor located in bladder, which presented with hematuria. Clinical diagnosis included submucosal cyst [11], vascular malformation, or unspecified benign lesion [12]. However, clinical differential diagnosis was not mentioned in the majority of the literature.…”

Rhabdomyoma of the pleura: a case report

“…The average onset age of fetal rhabdomyoma is 4 years and it occurs more commonly in males than females (ratio 2. A B C E D F submandibular region that is neither tender nor painful (5)(6)(7)(8).…”

The Juvenile Ribbons-Foetal Type Rhabdomyoma

“…Upon developing, individual myoblasts align and adhere to configure myotubes. On account of longitudinal proliferation, thickening of myofibrils and peripherally situated nuclei, myotubes evolve into muscle fibres which appear within the human embryo at around tenth week of development [3,4]. Classification of rhabdomyoma is contingent to clinical and pathological manifestations and is categorized as cardiac or extra-cardiac subtypes.…”

“…Extra-cardiac rhabdomyoma is subdivided into adult, foetal and genital subtypes. Exceptional instances of multi-centric rhabdomyoma can indicate a genetic pathogenesis although association of extra-cardiac rhabdomyomas with PTCH gene or pertinent genetic mutations remains unestablished [3,4].…”

“…Additionally, tumefaction can represent as a painless nodule or tumefaction at pertinent sites of tumour emergence. Clinically, the neoplasm may be associated site-specific symptoms such as hoarseness, difficulty in respiration or haematuria [3,4].…”