Faun Tail with Aplasia cutis congenita and Diastematomyelia

Aplasia cutis congenita associated with type I split cord malformation: Unusual case

“…[78] In our case, the spinal cord was split by a perpendicular bony spur and connected from its tip to the upper lamina. The spur was seen extending from the posterior border of the vertebral body and penetrating the anterior dura.…”

“…[3456] However, the association of ACC with SCM is considered very rare variant and only two reports of this condition are available. [78]…”

Aplasia cutis congenita: a rare cutaneous sign of split cord malformations

“…This correlation between hypertrichosis and SCM is probably higher than any other combination of cutaneous abnormality and underlying spinal cord lesion 2 . ACC is one of the cutaneous lesions associated with spinal dysraphisms and may present with faun tail in SCMs 5 …”

“…The cutaneous changes which may overlie an SCM have been reported previously, and include hypertrichosis, dysplastic skin, dermal sinus tract, subcutaneous lipoma, capillary hemangioma, vascular nevi, and hyperpigmentation 1–4 . Aplasia cutis congenita (ACC) is one of the rare cutaneous findings of SCMs, and is seldom reported in the literature 5 . According to the Frieden classification, 6 group 4 ACC is manifested by a hair collar overlying deeper embryologic malformations, such as myelomeningocele, porencephaly, spinal dysraphism, gastroschisis, and omphalocele.…”

Faun Tail Nevus and Spinal Dysraphism: Cosmetic Improvement with Alexandrite Laser Epilation

“…A proper evaluation with neurological and radiological examinations, may prevent possible sequels associated with spinal dysraphism1-4. In addition to the problems associated with spinal anomalies such as, back pain or incontinence, patient's physico-social life may be affected because of the localised hypertrichosis.…”