Extrarenal Angiomyolipomas of the Perinephric Space

Ditonno, P.; Smith, Robert B.; Koyle, Martin A.; Hannah, James; Belldegrun, Arie S.

doi:10.1016/s0022-5347(17)37266-x

Cited by 50 publications

(37 citation statements)

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“…Friis and Hjortrup reported the first ERAML (1982) in a 22-year-old female presenting with abdominal pain and weight gain who was found on exploratory laparotomy to have an 11 kg retroperitoneal AML [3]. Ditonno et al [4]have reported the largest series of ERAMLs, involving 40 cases. In their report, the liver was the most common extrarenal location (N = 18), followed by the uterus (N = 7), retroperitoneum (N = 4), and head and vagina (N = 2 each) as well as one each involving the penis, nasal cavity, hard palate, abdominal wall, fallopian tube, spermatic cord, and colon.…”

Section: Discussionmentioning

confidence: 99%

Retroperitoneal Angiomyolipoma: Rare Entity

Lokhande¹,

Goyal²,

Bhargava³

et al. 2017

APJHS

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Section: Discussionmentioning

confidence: 99%

Retroperitoneal Angiomyolipoma: Rare Entity

Lokhande¹,

Goyal²,

Bhargava³

et al. 2017

APJHS

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“…Asociaciones que no han sido observadas para los casos de AMLR. Su localizació n extrarrenal es extremadamente rara, siendo má s frecuente en el hígado, seguido del ú tero y la cavidad oral 2,6,10 . Presentamos el caso nú mero 19 de AMLR publicado en la literatura mundial, revisando su etiopatogé nia, clínica, diagnó stico, manejo y tratamiento.…”

Section: Actas Uroló Gicas Españ Olasunclassified

“…El crecimiento irregular por fuera de la fascia de Gerota, las calcificaciones intratumorales y el crecimiento mayor de 0,5 cm/añ o debe hacernos dudar del diagnó stico de benignidad 10,11,20 . Actualmente el valor de la arteriografía diagnó stica ha disminuido, y solo se recomienda para definir la vascularizació n y extensió n del tumor 6,10,23 . Para otros, ante aneurismas extrarrenales pequeñ os, con ramificació n arterial renal normal, deberíamos plantearnos la posibilidad de un AML extrarrenal.…”

Section: Actas Uroló Gicas Españ Olasunclassified

“…Sus características histoló gicas fueron inicialmente descritas por Fischer en 1911, asociado a esclerosis tuberosa o enfermedad de Bourneville donde suele ser bilateral, mú ltiple y de pequeñ o tamañ o 4,5 . La localizació n retroperitoneal es extremadamente rara, con solo 18 casos descritos hasta la actualidad en la literatura mundial (Cocharane Library, Ovid databases, Pubmed 1966-2009) [1][2][3][6][7][8][9][10][11][12][13][14][15][16][17][18][19] . Nuestro objetivo es revisar la literatura de esta patología, recopilando los casos descritos hasta la fecha, y presentar un nuevo caso de angiomiolipoma de origen retroperitoneal (AMLR) asociado al embarazo y puerperio.…”

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Angiomiolipoma retroperitoneal: revisión de la literatura y reporte de un nuevo caso

et al. 2010

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“…These tumours generally present within the kidneys, but there are reports in the literature of extrarenal AML, most commonly occurring in the liver and uterus. 1 Few reports have described an extrarenal extension of an AML.…”

Section: Introductionmentioning

confidence: 99%

A case of pararenal angiomyolipoma arising from an existing exophytic angiomyolipoma

Lipsky

Richardson

Tareen

2013

CUAJ

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A 52-year-old healthy woman with a congenital solitary right kidney presented with an incidentally found pararenal mass. Computed tomography and magnetic resonance imaging revealed an exophytic mass in the right kidney consistent with an angiomyolipoma and an additional enhancing pararenal mass that contained fatty elements. Differential diagnosis of the mass included liposarcoma and angiomyolipoma. Upon exploration, the exophytic angiomyolipoma was found to be contiguous with the pararenal mass via an isthmus of fatty tissue. Frozen sections were taken from both masses which confirmed that both were angiomyolipoma. This is the first case reported in the literature wherein an angiomyolipoma extended extrarenally and formed a significantly larger pararenal mass. Can Urol Assoc J 2010;4(3):E79-E81 IntroductionAngiomyolipoma (AML) is a benign tumour composed of fat, muscle and blood vessels. These tumours generally present within the kidneys, but there are reports in the literature of extrarenal AML, most commonly occurring in the liver and uterus. 1 Few reports have described an extrarenal extension of an AML.Two different types of AMLs have been described: fatpoor and classic. Fat-poor AML have been shown to evade radiographic diagnosis because of their lack of lipid component.2 While classic AML demonstrate all three components on histology, in certain cases one of the three constituents may dominate. Of note are the epithelial cell dominated AMLs, which are a more aggressive subtype that have the potential to metastasize.3 Some cases of AML can often be difficult to distinguish from liposarcoma, 4 as both types of tumours have fatty components. We report a case of a suspected angiomyolipoma in which a suspicious extrarenal extension of the mass prompted further investigation. Case reportA 52-year-old woman, with a history of microhematuria, was referred for evaluation of two suspicious renal masses on the right side. Past medical history was significant for a congenital solitary kidney. The patient had no other complaints and abdominal exam was benign. The results of laboratory studies including biochemistry and differential blood cell count were within normal limits. Abdominal computed tomography (CT) scan revealed a right renal mass and a right pararenal mass (Fig. 1a) (Fig. 1b). Magnetic resonance imaging studies confirmed that the pararenal mass enhanced with administration of contrast and also contained fatty elements (Fig. 2). The small exophytic renal mass was consistent with AML (Fig. 1b). The larger pararenal mass was more concerning; based on radiologic imaging it was difficult to determine whether the mass was a liposarcoma, which would require excision, or an AML which could simply be observed. It could not be determined whether the pararenal mass was in any way related to the exophytic AML.A CT-guided biopsy was considered but declined because of the significant risk of bleeding and also due to the potential for inconclusive diagnosis on fine needle aspiration. Also, due to the heightened c...

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Extrarenal Angiomyolipomas of the Perinephric Space

Abstract: We describe 2 cases of extrarenal angiomyolipoma of the perinephric space. All other cases of extrarenal angiomyolipoma of the retroperitoneum are reviewed and the clinical relevance of this unusual pathological entity is discussed.

Cited by 50 publications

References 20 publications

Retroperitoneal Angiomyolipoma: Rare Entity

Retroperitoneal Angiomyolipoma: Rare Entity

Angiomiolipoma retroperitoneal: revisión de la literatura y reporte de un nuevo caso

A case of pararenal angiomyolipoma arising from an existing exophytic angiomyolipoma

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