Extralobar Sequestration and Type II Congenital Cystic Adenomatoid Malformation in an Infant with Congenital Diaphragmatic Hernia

McManus, D.; Ohara, Maria

doi:10.1080/15513819609168699

Cited by 11 publications

(1 citation statement)

References 9 publications

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“…Other studies have reported associations of pulmonary sequestrations and CPAM with congenital diaphragmatic hernias and bronchogenic cysts [ 7 ]. The coexistence of separate anomalies in one lesion suggests that they are ends of a spectrum, rather than separate entities, and it has been suggested that it is more logical to describe all congenital cystic lung lesions as “congenital thoracic malformations” [ 8 ].…”

Section: Discussionmentioning

confidence: 99%

Coexistent Congenital Diaphragmatic Hernia with Extrapulmonary Sequestration

Kawamura

Bhandal

2016

Canadian Respiratory Journal

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Bronchopulmonary foregut malformations are a heterogeneous but interrelated group of abnormalities that may contain more than one histologic feature. It is helpful to be familiar with the presentation and imaging features of bronchopulmonary foregut malformations presenting as a congenital mass or mass-like lesion, as imaging plays a central role in the evaluation of these lesions since, when symptomatic, clinical features are usually nonspecific. With imaging, the presence of other associated lesions can be determined, facilitating appropriate management to prevent the potential complications. We report a case of coexisting extralobar pulmonary sequestration and ipsilateral diaphragmatic hernia in a term neonate.

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Section: Discussionmentioning

confidence: 99%

Coexistent Congenital Diaphragmatic Hernia with Extrapulmonary Sequestration

Kawamura

Bhandal

2016

Canadian Respiratory Journal

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Bronchopulmonary foregut malformations: embryology, radiology and quandary

Barnes

Pilling

2003

European Radiology

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Bronchopulmonary foregut malformations (BPFM) are a heterogeneous group of pulmonary developmental anomalies that present at varying ages and with overlapping symptoms, signs and radiology. This article discusses the embryology of these lesions with reference to possible common origins and the link between aetiology and radiological appearance. The radiology of each lesion, both antenatally and postnatally, is described and illustrated. A number of quandaries exist in the prediction of prognosis and subsequent treatment of BPFM. We discuss the radiological features that may help to elucidate an individual prognosis and aid in the planning of treatment. The treatment options available for BPFM are briefly discussed. Finally, the link between BPFM, in particular cystic adenomatoid malformations and malignancy, is discussed. We aim to provide a comprehensive overview of the embryology, radiology, prognosis and treatment highlighting contentious issues of BPFM.

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Extralobar Sequestration with Frequently Associated Congenital Cystic Adenomatoid Malformation, Type 2: Report of 50 Cases

1999

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Extralobar pulmonary sequestration (ELS) represents a mass of pulmonary parenchyma separate from the normal lung. The coexistence of congenital cystic adenomatoid malformation (CCAM) in ELS has been reported. To define this association, the clinical, gross, and histologic features of 50 ELS cases were analyzed. The age at diagnosis varied from birth to 65 years with 24% of cases diagnosed prenatally and 61% (23/38) diagnosed within the first 3 months of life. Fifty-two percent of cases were in females and 48% in males. Forty-eight percent of ELS(s) were located in the left hemithorax, 20% in the right hemithorax, 8% in the anterior mediastinum, 6% in the posterior mediastinum, and 18% beneath the diaphragm. The blood supply to the sequestration in 77% of cases was directly from the aorta. Grossly, the lung, though hypoplastic in some cases, was otherwise unremarkable. Fifty percent (23/46) of ELS cases were associated with a coexistent CCAM. In contrast to the series as a whole, 92% (11/12) of the ELS/CCAM cases, excluding those prenatally diagnosed, were diagnosed within the first 3 months and 57% occurred in females. ELS/CCAM lesions, while randomly distributed, were more frequently seen on the left side. Gross features of the ELS/CCAM cases were similar to those cases with ELS alone. All CCAM cases had a type 2 pattern on histologic examination with 48% of those cases also displaying rhabdomyomatous dysgenesis. Our findings indicate that the occurrence of CCAM in ELS is more frequent than reported in the literature and differs in presentation from ELS cases not associated with CCAM.

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Extralobar Sequestration and Type II Congenital Cystic Adenomatoid Malformation in an Infant with Congenital Diaphragmatic Hernia

Cited by 11 publications

References 9 publications

Coexistent Congenital Diaphragmatic Hernia with Extrapulmonary Sequestration

Coexistent Congenital Diaphragmatic Hernia with Extrapulmonary Sequestration

Bronchopulmonary foregut malformations: embryology, radiology and quandary

Extralobar Sequestration with Frequently Associated Congenital Cystic Adenomatoid Malformation, Type 2: Report of 50 Cases

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