Extragenital lichen sclerosus et atrophicus

Abstract

Lichen sclerosus et atrophicus (LSA) is a chronic inflammatory dermatosis with anogenital and extragenital presentations. Extragenital lichen sclerosus is most common on the neck, shoulders and upper trunk. Linear lesions are uncommon in LSA. We report a case of linear extragenital LSA involving forehead and scalp, along with grouped white papules of LSA in the right side of the back in a postmenopausal woman. The patient showed atypical clinical presentation of LSA in face which clinically mimicked ‘en coup de sabre’ as seen in morphea, but other clinical features suggested the diagnosis of LSA and the histopathological findings confirmed it.

Spontaneous regression of pediatric extragenital lichen sclerosus: A case report

“…LS is an inflammatory chronic dermatosis with anogenital and extragenital presentations 4 . It may occur in all ages with peak incidences in prepubertal and postmenopausal periods 2,5 .…”

Linear lichen sclerosus of the face

“…Extragenital lichen sclerosus (ELS) is most common on the neck, shoulders, and upper trunk. However, a linear distribution of ELS lesions is rare [3].…”

<p>Lichen sclerosus: the role of oxidative stress in the pathogenesis of the disease and its possible transformation into carcinoma</p>

“…In most cases (83–98% of cases) in both sexes LS affects the perianal and genital areas, more rarely it exclusively involves extragenital areas (neck, shoulders, trunk and back, buttocks, breasts, upper arms, axillae, umbilical region, wrists, nipples, face, around the ankles, palms and soles, etc. ); even more rarely, extragenital LS may affect the mucous membrane of the lips, mouth, and palate 1–3. Symptoms mostly include pruritus and pain at affected sites.…”

“…Even though certain age ranges are more exposed to the disease, LS can occur at any age. In females, LS incidence peaks at the periods in life with lower estrogen production (prepubertal and postmenopausal ages); even in males, the disease may affect both children and adults 1,3,6. It is difficult to determine the exact prevalence of LS for various reasons: very often, patients do not see a doctor, either because they have no symptoms or because they are ashamed or embarrassed, or LS is not diagnosed because patients present to specialists who are often not adequate for the type of disease 7.…”