Extra-Renal Wilm’s Tumor In A 3 Years Old Boy-A Case Report

Abstract

Wilm's Tumor, also known as nephroblastoma is mainly a malignant tumor of the kidneys. Extrarenal Wilm's is a rare entity and only few case reports are available in paediatric literature. We report the case of a 3 years old Pakistani boy who presented with abdominal mass in right upper and lower quadrant associated with pain. Abdominal tomography revealed a huge retroperitoneal mass compressing the right kidney & liver. Trucut biopsy of the mass revealed WT1 positive Wilm's tumor. He is currently on postoperative chemotherapy and is doing well.

Primary Extra-renal Wilms'Tumor in Urinary Bladder: Rare Presentation of a Common Pediatric Malignancy

“…Common sites of ERWT are retroperitoneum, inguinal canal, lumbosacral region, pelvis, mediastinum, chest wall, female genital tract, spermatic cord and the para-testicular region. [6][7][8][9][10][11] Majority of ERWT are located in the retroperitoneum. In this case, ERWT was present in the urinary bladder, a rare site for this tumor.…”

Extrarenal Wilms' Tumour of the Ovary

“…1 Extrarenal Wilms' tumour (ERWT) is rare with occasional reports. 1,2,3 The estimated incident rate of Extrarenal Wilms' tumour is almost 0.5 to 1% of all cases of Wilms' tumour. 2,3,4 Common reported location of Wilms' tumour outside the kidney included: retroperitoneum, inguinal canal, scrotum, and vagina.…”

“…1,2,3 The estimated incident rate of Extrarenal Wilms' tumour is almost 0.5 to 1% of all cases of Wilms' tumour. 2,3,4 Common reported location of Wilms' tumour outside the kidney included: retroperitoneum, inguinal canal, scrotum, and vagina. 4 Misdiagnosis for other common retroperitoneal masses of that region is not uncommon.…”