Extensive submandibular desmoid fibromatosis in a pediatric patient: A therapeutic challenge

Aggressive fibromatosis in the submandibular region of a child

“…Involvement of head and neck is not common, and there are case reports of infantile fibromatosis involving the submandibular space 3,11 . Clinical presentation of the lesion as a rapidly growing swelling was consistent with the reported cases of aggressive fibromatosis 3,12–14 . Despite negative sexual predilection, most of the reported cases of aggressive fibromatosis of the mandible were young females 3,11,12,14–17 .…”

“… 3 , 11 Clinical presentation of the lesion as a rapidly growing swelling was consistent with the reported cases of aggressive fibromatosis. 3 , 12 , 13 , 14 Despite negative sexual predilection, most of the reported cases of aggressive fibromatosis of the mandible were young females. 3 , 11 , 12 , 14 , 15 , 16 , 17 In the current case, lesion was mainly located in buccal and inferior portions of mandible and lingual vestibule showed normal depth, while bone destruction was observed in lingual aspect of the alveolar process away from the main tumor mass.…”

“… 3 , 12 , 13 , 14 Despite negative sexual predilection, most of the reported cases of aggressive fibromatosis of the mandible were young females. 3 , 11 , 12 , 14 , 15 , 16 , 17 In the current case, lesion was mainly located in buccal and inferior portions of mandible and lingual vestibule showed normal depth, while bone destruction was observed in lingual aspect of the alveolar process away from the main tumor mass. This kind of extension could be explained by periosteal extension of the lesion.…”