Extensive Slow-Flow Vascular Malformations and Pulmonary Hypertension

Venous malformations: Clinical course and management of vascular birthmark clinic cases

“…Most patients (85–88%) with large or extensive VM have LIC, and as a result it is suggested that these patients should undergo assessment and monitoring of their coagulation profile due to the risk of serious thrombohaemorrhagic coagulation disorders including disseminated intravascular coagulation (DIC) . Numerous case reports of PE and chronic thromboembolic pulmonary hypertension in both adults and children with KTS have been published . The incidence has not yet been established, however a case‐control study suggests that there is no significant difference in coagulation risks between extensive slow‐flow VM and KTS .…”