Ewing′s sarcoma of maxilla in an adolescent boy

Abstract

It is a rare malignancy that generally occurs in childhood. This tumor affects pelvic girdle and the long bones of the lower extremities commonly. CASE REPORTA 12-year-old male patient reported with a complaint of swelling since 4 months [ Figure 1] and pain for the past 1 month on the right side of the face. Swelling was of slow onset and progressive. Over a period of 4 months, the entire left side of ABSTRACT Ewing's sarcoma is a rarer malignancy, occurring usually in childhood. In majority of reported cases, the occurrence of this tumor is predominantly in the mandible than in the maxilla. Prognosis remains poor in most of the cases; however, better survival rate is possible with early diagnosis and combo therapy. A case of Ewing's sarcoma of the maxilla and its ramifi cations in the associated structures is presented here. We are also discussing complete clinical, radiographic, and histologic evaluation of the case.

Ewing’s Sarcoma of mandible in a pediatric patient: A case report

“…The characteristic 'sun-burst' or laminar periosteal "onion skin" reaction is a common radiological feature of ES involving long bones, but is rarely seen in jaws. [7][8][9] In the present case, the radiographic finding was an ill-defined osteolytic lesion associated with sun-ray spicules of periosteal bone. The radiographic findings were confirmed with CBCT scan and MRI in present case.…”

“…Systemic symptoms being fever, lymphadenopathy, weight loss, anemia, albuminuria are also observed. 8 Radiographically, it presents as an ill-defined osteolytic lesion with displacement of unerupted tooth follicles. The characteristic 'sun-burst' or laminar periosteal "onion skin" reaction is a common radiological feature of ES involving long bones, but is rarely seen in jaws.…”

“…3 Multidisciplinary treatment protocols have dramatically improved the 5-year survival rate of patients from 16 to 75%. [6][7][8][9] Radiotherapy can treat non resectable primaries and chemotherapy can suppress micrometastasis thus reducing tumour load before surgery. In our case, the patient underwent evaluation by a multidisciplinary tumor board that believed that the patient would have a good response to chemotherapy and could be treated with surgery before radiation therapy.…”

“…Previous studies supported the use of radiotherapy along with chemotherapy as an initial management option for large tumors (> 10 cm). 7,8,10 After resection of Ewing's sarcomas, large bone defects should be reconstructed to restore the function of affected limbs. The main options for reconstruction include autogenous bone grafts, allogeneic bone grafts and endoprosthesis.…”

Ewing′s sarcoma of mandible: A case report and review of Indian literature

“…[78] Prasad in 2008, Deshingkar and Gupta in 2009 and Dadhe in 2010 reported cases with extensive nasomaxillary destruction, proptosis of eye and decreased nasal airway competence. [412–14] Rao and Pampori in 2011 reported cases of ES involving mandible and maxilla, respectively. [15] Till date only 19 cases of ES involving jaws have been described in Indian literature.…”