Evaluation of the Consumption of Fruits and Vegetables by Phenylketonurics in the Metabolic Control of Phenylalanine: An Integrative Review

Preparation of food ingredients for the PKU patients: Two‐step enzymatic hydrolysis and activated carbon adsorption for the removal of phenylalanine from whey protein hydrolysates

“…Phenylalanine (Phe) is an essential amino acid that is metabolised to tyrosine in the liver by phenylalanine hydroxylase or its coenzyme tetrahydrobiopterin (Gao 2022). Phenylketonuria (PKU) is an autosomal recessive congenital metabolic defect caused by deficiency or decreased activity of PAH or its coenzyme tetrahydrobiopterin, which means increased Phe levels and decreased tyrosine levels in the blood (Minighin et al 2022). Untreated PKU patients may suffer from mental disabilities, neurological disorders, and even a shortened life expectancy (Van Spronsen et al 2021).…”