Evaluation of Cardiac Tumors in Children by Electron-Beam Computed Tomography Rhabdomyoma and Fibroma

Abstract

BackgroundThe most common cardiac tumors in young children are rhabdomyoma and fibroma, and prognosis depends on the tumor's characteristics. In the present study electron-beam computed tomography (EBT) was used to evaluate tumor characteristics and myocardial perfusion in 6 children with cardiac tumors. Methods and ResultsFive children had rhabdomyomas and 1 had a fibroma. In the precontrast study, the computed tomography numbers of rhabdomyomas were higher and those of the fibroma were slightly lower than those of the normal myocardium. In the early postcontrast study, the size, location, shape and number of the tumor were clearly detected, and in the late postcontrast study, the fibrous characteristics of the tumor were seen. The fibroma contained calcification and 2 rhabdomyomas contained a fat density spot. In the cine-mode study, both the tumor and ventricular wall motion could be simultaneously evaluated. There was a filling defect of the left ventricular myocardium on the early postcontrast scan of 1 child with a rhabdomyoma and dyskinetic wall motion at the same region in the cine-mode study. Conclusion EBT was useful for evaluating tumor characteristics in children. (Circ J 2005; 69: 1352 -1356

Rabdomioma cardiaco en relación con tetralogía de Fallot y esclerosis tuberosa

“…La RM cardiaca se reserva para pacientes seleccionados en los que el tipo de tumor es cuestionable después de la ecocardiografía o se requiere información anatómica o funcional adicional 21 . La RM también es útil como estudio de extensión, ya que permite evaluar lesiones características de esclerosis tuberosa en otros órganos, como el cerebro, el hígado y los riñones, que pueden verse afectados.…”

“…La RM también es útil como estudio de extensión, ya que permite evaluar lesiones características de esclerosis tuberosa en otros órganos, como el cerebro, el hígado y los riñones, que pueden verse afectados. En el caso reportado se documentaron nódulos subependimarios en el sistema ventricular lateral, lo que permitió confirmar el diagnóstico de esclerosis tuberosa e iniciar el acompañamiento por parte del servicio de neurología pediátrica [19][20][21][22] .…”

A prenatally diagnosed newborn with an intracardiac rhabdomyoma obstructing the left ventricular outflow tract

“…Multipl oluşu, miyokard dokusundan daha hiperekojen görünmesi rabdomiyom olduğunu düşündürmekle birlikte fibroma, teratoma gibi çocukluk çağında görülen diğer intrakardiyak tümörlerden ayırım için bilgisayarlı tomografi, manyetik rezonans görüntüleme gibi diğer tanı yöntemlerine başvurmak gerekebilir. [6] Olgumuzda her iki ventrikülde de lezyon saptanmış olması, miyokarddan daha hiperekojen görülmesi nedeni ile öncelikli olarak rabdomiyom düşünüldü ancak tanı ameliyat sonrası patolojik değerlendirme ile kesinleştirilebildi. Sağ ventrikül içindeki kitlelerin küçük boyutlu oluşu, atriyoventriküler ve semilüner kapaklara etkilerinin olmayışı nedeniyle cerrahi olarak çıkarılmadı.…”