Esophageal lung with rare associated vascular and anorectal malformations

Alsaadi, Ali; Alsufiani, Hamdi; Allugmani, Mohammad D.; Gora, Altaf Hussain

doi:10.1016/j.radcr.2018.01.029

Cited by 11 publications

(14 citation statements)

References 17 publications

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“…The subsequent surgical options include either the connection of the unventilated lung to the respiratory tree through a bronchotracheal anastomosis, or a pneumonectomy. In most case report, the treatment of choice is pneumonectomy, 1 2 3 4 5 6 7 8 but there are reports of successful tracheobronchial reconstructions. 9 10 11 In our case, we judged that a tracheobronchial anastomosis was unfeasible due to the long tracheobronchial gap, in fact the position of the right main bronchus was very low in the thorax with a gap of four vertebral bodies between its origin and the end of the trachea, as it is well evidenced by the three-dimensional CT reconstruction of the anatomy of our patient ( Fig.…”

Section: Discussionmentioning

confidence: 99%

Possible Approach to Esophageal Lung with Long Tracheobronchial Gap

Ichino

Pugni

Zanini

et al. 2019

European J Pediatr Surg Rep

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Esophageal lung is a rare bronchopulmonary foregut malformation characterized by an anomalous origin of one of the main bronchi which arises from the esophagus. Less than 30 cases are reported in the literature. Therefore, there are no standardized guidelines for the treatment of this condition. We report a case of right esophageal lung diagnosed in a neonate. The patient was treated with thoracoscopic closure of the ectopic main bronchus in the neonatal period, followed by delayed pneumonectomy at 5 months of age. No prosthetic substitute was implanted in the ipsilateral hemithorax after pneumonectomy. The patient is now 4 years old and doing well, postpneumonectomy syndrome was never observed. Our strategy and the possible alternatives are discussed here.

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Section: Discussionmentioning

confidence: 99%

Possible Approach to Esophageal Lung with Long Tracheobronchial Gap

Ichino

Pugni

Zanini

et al. 2019

European J Pediatr Surg Rep

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“…Initially, resection has been described for management of abnormal communicating tissue in addition to removal of the hypoplastic lung that has been destroyed by recurrent infections; with repairing of the esophageal communication. 16 17…”

Section: Discussionmentioning

confidence: 99%

Esophageal Lung in a Preterm Boy—Report on a Multidisciplinary Treatment

Villamizar

Pedraza

et al. 2019

European J Pediatr Surg Rep

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Esophageal lung is a rare entity that results from embryological alterations during the formation of the ventral wall of the anterior intestine. The clinical manifestations of this pathology are vague, including respiratory or digestive symptoms, repetitive respiratory infections, dysphagia, or inability to swallow. The management is based on the exact anatomical and vascular abnormalities. We report the diagnostic and therapeutic approach in a preterm boy with esophageal lung. Also, we present a three-dimensional model for the classification of this pathology. In conclusion, the management relies on proper definition of the anatomy and the surgical strategy.

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“…Fewer than 30 cases of esophageal lung have been reported in the literature. 2 This report describes a case of esophageal lung associated with VACTERL abnormalities.…”

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confidence: 94%

Management of Esophageal Lung in a Patient With VACTERL Anomalies

Harrell

Moss

Bhattacharya

et al. 2020

The American Surgeon

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Esophageal lung is a rare type of bronchopulmonary foregut malformation where an anomalous main bronchus arises from the esophagus rather than the trachea. This differentiates from an esophageal bronchus where a lobar bronchus arises from the esophagus. Fewer than 30 of these anomalies have been reported in the literature. A female infant was born at 35 weeks gestational age and found to have multiple congenital abnormalities including cleft palate, long-gap esophageal atresia, tracheoesophageal fistula (TEF), imperforate anus, and renal anomalies. She initially underwent thoracoscopic ligation of TEF with colostomy and mucus fistula creation. Bronchoscopy found no right mainstem bronchus, and subsequent computed tomography scan was consistent with possible esophageal bronchus. Esophagoscopy through the gastrostomy discovered a fistulous connection between the distal esophagus and anomalous main right bronchus. Right thoracotomy with pneumonectomy of the hypoplastic lung was performed. She subsequently underwent vaginostomy for hydrometrocolpos. Her proximal esophagus was diverted with a cervical esophagostomy for control of secretions. She also required tracheotomy and is currently at home on minimal ventilator settings awaiting staged reconstruction. Esophageal lung is a rare congenital abnormality with few reported cases. Surgical treatment with pneumonectomy is often required, and pediatric surgeons should be familiar with these congenital bronchopulmonary malformations.

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Esophageal lung with rare associated vascular and anorectal malformations

Cited by 11 publications

References 17 publications

Possible Approach to Esophageal Lung with Long Tracheobronchial Gap

Possible Approach to Esophageal Lung with Long Tracheobronchial Gap

Esophageal Lung in a Preterm Boy—Report on a Multidisciplinary Treatment

Management of Esophageal Lung in a Patient With VACTERL Anomalies

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