“…Cabrera et al [12] reported an 11-year-old boy with developmental delay, mental retardation, dyskinesias, ear malformations and hypertonia of the left leg, who presented pigmented macules over the left abdomen and limbs, among which an oval-shaped SLN with terminal hairs on the left thigh was described. Garrido-Arredondo et al [13] documented a white patient affected by a large hairy SLN on the left supraclavicular/deltoideal region and idiopathic scoliosis. However, the lack of important data as well as some unfitting features prevent one from labeling the overmentioned patients with sine dubio SLN syndrome.…”