Érythème nécrolytique migrateur au cours d’une maladie de Waldmann

Baricault, S.; Soubrane, J; Courville, Philippe; Young, Paul R.; Joly, P.

doi:10.1016/s0151-9638(06)70994-2

Cited by 6 publications

(1 citation statement)

References 15 publications

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“…Chyle can also backflow into the skin of the lower limb, perineum or external genitalia [7] and necrolytic migratory erythema may be seen [8]. The yellow nail syndrome is another rare condition which may be associated with PIL; dystrophic yellow nails with ridging and loss of lunula on the hands are associated with lymphedema and pleural effusions [9].…”

Section: Introductionmentioning

confidence: 99%

Digital clubbing in primary intestinal lymphangiectasia: a case report

Wiedermann

Kob

Benvenuti

et al. 2010

Wien Med Wochenschr

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Primary intestinal lymphangiectasia (PIL), also known as Waldmann's disease, is a rare disorder characterized by dilated intestinal lacteals resulting in lymph leakage into the small bowel lumen and responsible for protein-losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. The symptoms usually start in early infancy. We report a case of secondary hyperparathyroidism, osteopenia, monoclonal gammopathy and digital clubbing in a 57-year-old patient with a 12-year history of discontinuous diarrhea. Malabsorption with inability to gain weight, and finally weight loss and formation of leg edema were associated with protein-losing enteropathy. A low-fat diet associated with medium-chain triglyceride supplementation was clinically effective as medical management in reducing diarrhea and leg edema, and promoting weight gain. Double-balloon enteroscopy and small bowel biopsy histopathology confirmed dilated intestinal lacteals. Digital clubbing associated with primary intestinal lymphangiectasia which may causally be related to chronic platelet excess has not been reported before.

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Section: Introductionmentioning

confidence: 99%