“…With anomaly it is highly unusual for a patient to survive without surgical interventional, because there would be no path for the blood to leave the heart and enter the systemic circulation [3] . Nonetheless, this condition has been identified later in adult life in rare cases [5] , [10] , [11] , [12] , [13] , [14] . Patients with isolated IAA may survive until adulthood due to the development of significant collateral circulation ensuring the maintenance of a blood flow to the distal aorta [7] , [15] , [16] , as in our patient, who had important collateral circulation and had an associated bivalve aorta observed on the CTA.…”