Epithelioid hemangioendothelioma of parapharyngeal space: A rare clinical entity

Abstract

Introduction: An epithelioid hemangioendothelioma is a rare vascular neoplasm primarily of lung, liver, and bones. It is regarded as a neoplasm of borderline or low-grade malignant potential uncommonly seen in head and neck region. It may manifest in other parts of body like breast, lymph nodes, mediastinum, brain, meninges, spine, skin, abdomen, and many other sites. Due to its heterogeneous presentation, rarity, and malignant potential, it is often misdiagnosed and not adequately treated.Case Report: We herein present a case of hemangioendothelioma of parapharyngeal space in an adult male with progressive swelling in right cervical region. Involvement of parapharyngeal space by this tumor is very rare, which warrants reporting of this case. The dumbbell-shaped tumor was surgically excised in toto and histopathology confirmed the diagnosis. Conclusion:A wide surgical excision and regular follow-up would be appropriate management. Further research and studies are needed to formulate standardized treatment protocols for this rare tumor.