Epithelial ovarian tumor in a phenotypic male

Abstract

Laparotomy in a 41-year-old married man with non-treated left cryptorchidism revealed female internal genitals on the left side, and an epithelial ovarian tumor of intermediate malignancy. Germinal malignancies are frequent in intersexes, but non-germinal gonadal neoplasms are rare. This is the second reported case of epithelial ovarian tumor in intersexes, and the first case of epithelial ovarian tumor in an intersex registered as male.

Ovarian Epithelial Tumour in Gonadal Dysgenesis A Case Report and Literature Review

“…Ovarian epithelial tumours such as serous or mucinous tumours are very rare in patients of gonadal dysgenesis. There have only been 7 reported cases in the literature (4)(5)(6) and the present case presented is the eighth.…”

Laparoscopic Surgery in 46,XX Disorder of Sex Development: Hysterosalpingectomy with Gonadectomy

“…There are only rare reports of ovarian tumor, such steroid cell tumor and epithelial tumor, in this group of patients. 8,9 Little is known about the long-time consequences of rising 46,XX DSD as male. The ethical aspects are unresolved in these cases.…”