Epidural dumbbell-shaped chordoma mimicking a neurinoma

Abstract

The authors present a case of cervical chordoma which manifested in a 5-year-old boy as a dumbbell-shaped epidural tumor without bone destruction. Both CT and MRI demonstrated tumor features suggesting this diagnosis, which was confirmed by histology.

A Case Report of Chondrosarcoma That Primarily Developed in the Cervical Spine

“…A case report of dumbbell-shaped lymphangioma, a case report of dumbbell-shaped chordoma and another case of lipoma have also been documented [2][3][4]. …”

Cervical chordoma with vertebral artery encasement mimicking neurofibroma: MRI findings

“…The appearance of ad-vanced lesions is that of vertebral destruction with soft tissue extension. Involvement of the intervertebral disks, enlargement of the neuroforamen, and calcified deposits are often seen [1,3,6]. Such calcifications were not seen in our case.…”

“…Approximately 2-4 % of chordomas are benign. Since they respond poorly to irradiation and chemotherapy, extensive resection is desirable but often impossible because of the extent of the tumor at presentation and because of several anatomical constraints [1,2,3,4,5,6]. The recurrence rates are high and the prognosis is poor with few patients surviving longer than 5 years [5,7].…”

Neural Foraminal Lesions: An Imaging Overview

“…Nearly 50% of chordomas are located in the sacrococcygeal region, 35% in the spheno‐occipital clival synchondrosis, and the remaining within spinal vertebrae [12]. A few case reports have described neural foramen extension of chordomas presenting with compression through the neural foramina in a longitudinal fusiform manner [13].…”