Epidemiological study of hearing impairments in children: prevalence, structure, amplification, and social factors

Tufatulin, G.Sh.; Королева, И. В.; Mefodovskaya, E K

doi:10.17116/otorino20218603128

Cited by 6 publications

(1 citation statement)

References 16 publications

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“…After CI the EABRS were not recordable in our patients, speech recognition was poor. These data and patophisiology of TWNK related disorders, which is based on axonopathy, lead to conclusion, that TWNK-related ANSD cause auditory neuropathy type of ANSD [40].…”

Section: Other Syndromes With Ansdmentioning

confidence: 81%

Auditory Neuropathy Spectrum Disorder: Genetic and Electrophysiological Testing for Predicting Rehabilitation Outcomes after Cochlear Implantation

Lalayants¹

2023

Latest Advances in Cochlear Implant Technologies and Related Clinical Applications

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Reviling the etiology or at least pathophysiology of auditory neuropathy spectrum disorder is crucial for choosing rehabilitation pathway and predicting rehabilitation outcomes. Some patients with auditory neuropathy spectrum disorder undergo cochlear implantation, but it is not always possible to foresee the results of rehabilitation. Genetic testing, especially in cases without obviously perinatal hearing loss risk factors, might help to understand etiology and pathophysiology, whether it is synaptopathy or neuropathy; therefore, it becomes possible to predict rehabilitation outcomes. More than 20 genes related to auditory neuropathy spectrum disorder phenotype are known already. Modern genetic approaches, such as whole genome and whole exome sequencing, reveal etiology of auditory neuropathy spectrum disorder in many cases. But there are still auditory neuropathy spectrum disorder cases with unknown etiology and site of the lesion. Electrophysiological methods (electrocochleography, electrically evoked brainstem potentials) might help to localize the site of lesion in hearing system and therefore help to predict rehabilitation outcomes. Electrically evoked brainstem potential testing after cochlear implantation seems to be applicable and useable tool to predict potential CI outcomes and to choose optimal rehabilitation trace.

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Section: Other Syndromes With Ansdmentioning

confidence: 81%

Auditory Neuropathy Spectrum Disorder: Genetic and Electrophysiological Testing for Predicting Rehabilitation Outcomes after Cochlear Implantation

Lalayants¹

2023

Latest Advances in Cochlear Implant Technologies and Related Clinical Applications

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Study of Factors Influencing Medical, Psychological and Pedagogical Rehabilitation Efficacy in Preschool Children with Hearing Disorders

Tufatulin

2021

Pediatr. farmakol.

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Objective. The aim of the study is to identify the most significant factors influencing the audio-verbal rehabilitation outcomes in preschool children.Methods. The study included 104 children, 3–7 years of age, with hearing loss who underwent course of audioverbal rehabilitation in audiology center: 50 children after cochlear implantation, 51 children with hearing aids, 3 children without hearing care. The following data was collected at the beginning of the course: gender, type and degree of hearing loss, comorbidities, method and age of hearing care, family structure, preschool organization type. The scale of social and psychological diagnostics was filled in. The dynamics of indicators were estimated at the end of the course. The overall result was rated as high, good, medium or low. Correlations between clinical, audiological, social, psychological data and different rehabilitation outcomes were estimated.Results. Degree and type of hearing loss, method of hearing care, gender, age, and social aspects do not affect the rehabilitation outcomes. Hearing aid was performed before 3 years of age in 67% of children, and after 3 years of age in 33% of children in the group with high and good results. Hearing aid was performed after 3 years of age in 61% of children, and before 3 years of age in 39% of children in the group with medium and low results (p < 0.01). Burdened anamnesis and comorbidity was determined in 28% of children with high/good outcomes and in 59% of children with medium/low outcomes (p < 0.01). Children with medium results rarely have previous audiology therapy, 43.8% of cases (p < 0.01). Children with medium and low outcomes have statistically worse score according to the scale of social and psychological diagnostics (p < 0.05 and p < 0.01, respectively).Conclusion. High results of audio-verbal rehabilitation in preschool children can be predicted by the age of primary hearing care (before 3 years of age), absence of comorbidities, previous audiology therapy, score at the scale of social and psychological diagnostics less than 17 points.

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Hearing loss due to mutations in the genes responsible for Usher syndrome

Маркова¹,

Alekseeva²,

Belov³

et al. 2022

Vestn. otorinolaringol.

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Epidemiological study of hearing impairments in children: prevalence, structure, amplification, and social factors

Cited by 6 publications

References 16 publications

Auditory Neuropathy Spectrum Disorder: Genetic and Electrophysiological Testing for Predicting Rehabilitation Outcomes after Cochlear Implantation

Auditory Neuropathy Spectrum Disorder: Genetic and Electrophysiological Testing for Predicting Rehabilitation Outcomes after Cochlear Implantation

Study of Factors Influencing Medical, Psychological and Pedagogical Rehabilitation Efficacy in Preschool Children with Hearing Disorders

Hearing loss due to mutations in the genes responsible for Usher syndrome

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