Epibulbar Osseous Choristoma and Ectopic Lacrimal Gland Underlying a Dermolipoma

Abstract

A 6-month-old girl underwent surgical excision of an epibulbar mass which had the clinical appearance of a dermolipoma. Intraoperatively, a separate underlying mass was uncovered which was firmly adherent to the sclera. Histopathologic examination confirmed the superficial lesion to be a typical dermolipoma, and the underlying lesion to be an epibulbar osseous chroistoma with associated adherent ectopic lacrimal gland tissue. The clinical features, management, and histopathology of this new association are reviewed.

Epibulbar osseous choristoma with dermolipoma: A case report and review of literature

“…Full-text, free-access, Englishprinted articles with pathologically confirmed epibulbar osseous choristoma and dermolipoma identified 14 cases (Table 1). [8,[11][12][13][17][18][19][20][21][22][23][24][25][26][27] Including our case, age range at presentation was from birth to 38 years with mean age of 11.6 years. Ten cases (66.7%) were females, and 5 cases (33.3%) were males.…”

“…In review of literature, CT images of epibulbar osseous choristoma revealed a cystic mass with fat-like low-density and a high-density radio-opaque mass which is indicative of a calcium component. [8,11,12,[17][18][19][20][21][22][23][24]26] This differentiates epibulbar osseous choristoma from low-density lesions like fat, dermolipoma, or epibulbar dermoid and helps predict the diagnosis.…”

“…We conducted a systematic literature review on previously reported cases via PubMed using the keywords “congenital subconjunctival mass,” “epibulbar osseous choristoma” and “epibulbar dermolipoma.” Full-text, free-access, English-printed articles with pathologically confirmed epibulbar osseous choristoma and dermolipoma identified 14 cases (Table 1). [8,11–13,17–27] Including our case, age range at presentation was from birth to 38 years with mean age of 11.6 years. Ten cases (66.7%) were females, and 5 cases (33.3%) were males.…”

“…Khan et al [12] 2 M OD Lateral canthus Excision Mature bone with adipose tissue No No 13 Casady et al [24] 18m M OD Lateral canthus Excision Irregular collagen similar to dermis with adipose tissue and mature lamellar bone inside…”