Microespherocytosis in PediatricsMicroespherocitosis is the most comon hereditary anemia. Clinically it is caracterized for haemolytic anemia, with jaundice and transfusional requirements, sympthoms can be more intense in newborn period. With the purpose of review this disease, we studied the patients of the pediatric haematology policlinic in Roberto del Río Hospital, controlled between 1990 to 2005, we check the patient`s records and registerd the clinic and family background evaluating through the Eber's severity classifi cation the indication of splenectomy in each case. We registerd 44 patients. The 68.2% had family background. The 77.3% presented sympthoms during the newborn period, in wich 91.2% had jaundice. The 38.6% needed at least one transfusion after the newborn period. The Eber's severity classifi cation was different according to the variable evaluated, wich made its aplication diffi cult. Only one of the nine splenectomized patient had this indication. From the year 2000 the inquiry of the disease as well as the correct indication of splenectomy has improved. This coincides with the appearance of the Eber's publication about this disease. Conclusion: Microespherocitosis usually appears in the newborn period as jaundice and most patients has familial antecedents. Eber's severity classifi cation and molecular study allows a rational splenectomy indication and predicts the disease evolution.
RESUMENLa microesferocitosis es la anemia hemolítica más frecuente en pediatría. Se caracteriza por asociarse a ictericia y requerir transfusiones, y la sintomatología puede ser más acentuada en período de recién nacido.