Enterocolitis in the evolution of an early diagnosed Hirschsprung disease - case report

Abstract

Hirschsprung disease associated enterocolitis (HAEC) represents a recognized complication with multifactorial etiology, remaining a leading cause of morbidity and mortality among infants with Hirschsprung disease. This report describes the case of an infant boy with a history of delay in meconium passage and bilious vomiting at 2 days of age, presenting at a subsequent admittance with presumptive suboclusive syndrome, which turns out to be after rigorous investigations a Hirschsprung disease complicated with enterocolitis. The case highlights the importance of prompt recognition and energetic intervention for HAEC, which together with choosing the appropriate surgical approach leads to a beneficial outcome in patient's evolution.