Enteritis Cystica Profunda Presenting as Ileoileal Intussusception in a Child: Report of a Case

Abstract

We report the case of a 3-month-old male infant with small bowel intussusception caused by enteritis cystica profunda (ECP). The baby was admitted because he was refusing to feed, and was passing "red-currant jelly"-like stools. A palpable mass was identified, and abdominal ultrasonography showed a mass with a lumen and lumen appearance. We performed laparotomy and resected the segment of bowel containing the mass. The resected segment had enteritis cystica profunda, which was considered to have precipitated the intussusception. A review of the English medical literature revealed only three other cases of children with similar symptoms in the last 30 years.

A case of pneumatosis cystoides intestinalis complicated by intussusception

“…Surgical treatment is performed in rare cases involving patients who do not respond to conservative management, 1,2 and operation is required in rare cases with bowel perforation or non-operative reduction of intussusception. 3,5 In our case, the patient had severe motor and intellectual disabilities, cardiac malformation, chronic respiratory failure and developmental delay. He had suffered from hard constipation and aerophagia for a long timeunderlying conditions that might be favorable for PCI.…”

“…Most cases are successfully treated with conservative management, such as antibiotics, high‐flow oxygen and / or hyperbaric oxygen treatment. Surgical treatment is performed in rare cases involving patients who do not respond to conservative management, 1,2 and operation is required in rare cases with bowel perforation or non‐operative reduction of intussusception 3,5 …”

Colitis Cystca Profunda causing colo-colic intussusceptions in an adult

“…CCP is often mistaken for mucinous carcinoma and invasive carcinoma. Ilio-ileal intussusceptions in child caused by enteritis cystica profunda have been reported [8].…”

Intussusception

“…We have observed a jejunojejunal I due to an intes- tinal metastasis in a 14-year-old boy with a pulmonary sarcoma extending into the superior vena cava and multiple cerebral and renal metastases. Enteritis cystica profunda, a very uncommon condition, characterized by non-neoplastic cystic spaces within the small bowel wall has been reported as a cause of I (Karnak et al 1997;Sunagawa et al 2005).…”