Enlarged vestibular aqueduct: Intraoperative electrocochleography findings during cochlear implantation

Predictive accuracy of wideband absorbance in children with large vestibular aqueduct syndrome: A single-center retrospective study

“…Large vestibular aqueduct syndrome (LVAS) is a prevalent congenital anomaly of the inner ear that results in early-onset Sensorineural Hearing Loss (SNHL) [ [1] , [2] , [3] , [4] ]. LVAS accounts for approximately 13–15 % of pediatric SNHL cases [ [5] , [6] , [7] ].…”

“…LVAS accounts for approximately 13–15 % of pediatric SNHL cases [ [5] , [6] , [7] ]. The majority of LVAS cases (81–94 %) show bilateral SNHL, which can be fluctuating and/or progressive, and is frequently accompanied by vestibular impairment, such as episodic vertigo or postural instability [ 1 , 8 ]. Factors that elevate intracranial pressure, such as viral infections, head trauma, or emotional stress, can precipitate sudden hearing loss and/or vertigo in LVAS patients [ 9 ].…”