Endomiocardiofibrose biventricular associada à amiloidose renal

Abstract

Endomyocardiofibrosis is a restrictive cardiomyopathy characterized by fibrotic involvement of the endocardium and adjacent myocardium, and by diastolic dysfunction caused by changes in distensibility making ventricular filling inadequate while preserving the systolic function. Clinically, it appears as heart failure, but etiological symptomatic discernment, suspicion and a clinical examination would be necessary in order to make a correct etiological diagnosis. The case of a patient with biventricular endomyocardial fibrosis associated with renal amyloidosis is presented.

Cardiologia Teoria e Prática - Edição XIV

“…Nas formas avançadas, a EMF pode levar à morte, principalmente por insuficiência cardíaca congestiva ou arritmias malignas. Apenas 22% dos pacientes apresentam sintomas (WAGNER et al, 2019;RAMOS FILHO et al, 2005;SOARES et al, 2023).…”