Emergency Dental Treatment of a Patient With Sturge-Weber Syndrome

Abstract

The Sturge-Weber (SWS) syndrome is a rare condition with congenital capillary malformations. Hemorrhages may occur on dental treatment, which can have a dramatic effect on a patient's vital sign. The aim of the present brief clinical study was to briefly report a case of a female patient with SWS who underwent an endodontic treatment. A 25-year-old patient (C.O.B.S.) with SWS and vascular malformation in cervicofacial right region was admitted to the dental clinic with pulsatile pain in tooth 16. An emergency dental treatment with cavity preparation and access to root canals was performed with intraligamentary and intrapulpal anesthesia with 3% prilocain 3% with felypressin 0.03 UI/mL because the tooth was located in the region of the vascular malformation, and any surgical treatment could lead to hemorrhages. After 7 days, the patient was recalled with the absence of painful symptoms. The endodontic treatment in patients with SWS is feasible, and safety should be an alternative to surgical treatments.

Surgical Management of Odontogenic Infection in Sturge–Weber Syndrome: Report of a Case

“…Sturge–Weber Syndrome (SSW) is a neurocutaneous disorder associated with capillary malformation in facial region, glaucoma and leptomeningeal angioma, 1 first described by Schirmer in 1860 and later by Sturge in 1879. Although rare, the SWS is the third most common neurocutaneous syndrome, after type 1 neurofibromatosis and tuberous sclerosis 2,3,8 . Intraoral involvement is common, being present in about half of the cases, resulting in ipsilateral changes in the oral mucosa.…”

“…Although rare, the SWS is the third most common neurocutaneous syndrome, after type 1 neurofibromatosis and tuberous sclerosis. 2,3,8 Intraoral involvement is common, being present in about half of the cases, resulting in ipsilateral changes in the oral mucosa. Pontes et al 3 suggest that affected mucosa is hypervascularized and minor trauma can lead to intense bleeding.…”