Embryonal rhabdomyosarcoma of the ampulla of Vater in early childhood: report of a case and review of literature

Perera, M Thamara P R; McKiernan, Patrick; Bründler, Marie-Anne; Hobin, David; Mayer, David; Mirza, Darius F.; Sharif, Khalid

doi:10.1016/j.jpedsurg.2008.10.113

Cited by 15 publications

(11 citation statements)

References 12 publications

(13 reference statements)

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“…Median age at presentation is 3 years, but it should be included in the differential diagnosis of an infant presenting with jaundice and a mass in the porta hepatis. Other diagnostic possibilities include undifferentiated sarcoma of the liver, pancreateoblastoma, papillary cystic tumor of the pancreas, metastatic lesions and more rarely, hepatoblastoma [50,51] . Additionally, a RMS in this location can mimic the radiological appearance of a choledochal cyst because of its combined cystic and solid component [52] .…”

Section: Biliary Tract Rhabdomyosarcomamentioning

confidence: 99%

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Differential diagnosis and management of liver tumors in infants

Fernández-Pineda

Cabello-Laureano

2014

WJH

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During the first year of life, most of the liver neoplasms are benign in origin, but some of these histologically benign lesions may be challenging in their management. Although most hepatic hemangiomas can be safely observed until involution is documented, some patients will need treatment due to progressive hepatomegaly, hypothyroidism and/or cardiac failure. Large mesenchymal hamartomas may require extensive hepatic resection and an appropriate surgical plan is critical to obtain good results. For malignant neoplasms such as hepatoblastoma, complete surgical resection is the mainstay of curative therapy. The decision about whether to perform an upfront or delayed resection of a primary liver malignant tumor is based on many considerations, including the ease of resection, surgical expertise, tumor histology and stage, and the likely chemosensitivity of the tumor. This article reviews the initial management of the more common hepatic tumors of infancy, focusing on the differential diagnosis and treatment options.

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Section: Biliary Tract Rhabdomyosarcomamentioning

confidence: 99%

“…Multiagent neoadjuvant chemotherapy following the biopsy may avoid important complications associated to a massive primary resection. Even after chemotherapy, gross total resection is rarely possible but outcome is good despite residual disease after second-look surgery [48,51] .…”

Section: Biliary Tract Rhabdomyosarcomamentioning

confidence: 99%

Differential diagnosis and management of liver tumors in infants

Fernández-Pineda

Cabello-Laureano

2014

WJH

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“…El tumor relacionado con el quiste de colédoco es el colangiocarcinoma, y es extremadamente raro un quiste de colédoco con histología de rabdomiosarcoma; solo existen unos pocos pacientes reportados en la literatura 5,10 . La presentación clínica típica es ictericia obstructiva con o sin distensión abdominal, fiebre y anorexia; puede existir extensión al hígado y al retroperitoneo o pulmones.…”

Section: Discussionunclassified

“…Generalmente la ictericia se refleja con elevación moderada de bilirrubinas directas e indirectas. Puede estar elevada la fosfatasa alcalina y TGO 10,16 .…”

Section: Discussionunclassified

Reporte de caso. Rabdomiosarcoma botrioides de la vía biliar

Lizcano¹,

Navarro²,

Avelino³

et al. 2016

Imagen Diagnóstica

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Recibido el 10 de marzo de 2015; aceptado el 7 de mayo de 2015 Disponible en Internet el 6 de noviembre de 2015 PALABRAS CLAVEQuiste de colédoco; Rabdomiosarcoma de la vía biliar Resumen El rabdomiosarcoma de la vía biliar es un tumor raro en niños. Tiene un pobre pronóstico, y representa alrededor del 8% de todos los cánceres en niños menores de 15 años. El sitio más comúnmente involucrado incluye cabeza y cuello (36%). Raramente se encuentra en víscera hueca: laringe, bronquios, intestino delgado y tracto biliar, y de manera frecuente se confunde con quiste de colédoco. A su vez, es el tumor más frecuente de la vía biliar: representa el 1% de todos los rabdomiosarcomas y aproximadamente el 0,04% de todos los tumores en niños. La apariencia radiológica es similar al quiste de colédoco cuando no existe extensión a órganos vecinos. En la tomografía axial computarizada la densidad de este tumor es menor que la del hígado y semeja un tumor quístico. El objetivo es reportar el caso Abstract Rhabdomyosarcoma (RMS) of the biliary tract is a rare tumour in children. It has a poor prognosis, and represents about 8% of all cancers in children younger than 15 years. The most commonly involved site includes head and neck, with 36%. Rarely found in viscera larynx, bronchi, small intestine and biliary tract, frequently confused with choledochal cysts, and in turn is the most common tumour of the bile duct, and represents 1% of all rhabdomyosarcomas, and about 0.04% of all tumours in children. The radiological appearance is similar to choledochal cyst when there is no extension to adjacent organs. In computed tomography, the density of this tumour is less than the liver and resembles a cystic tumour. The aim of the article is to report the cases in the 'Eva Samano Lopez Mateos' Children's Hospital.

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“…[2] Given the rarity of this disease, the majority of the pediatric literature consists of isolated case reports. [3][4][5][6][7] We present a case of a child with biliary RMS initially diagnosed as a choledochal cyst on radiologic imaging.…”

Section: Introductionmentioning

confidence: 99%

Rhabdomyosarcoma arising within the biliary tract mimicking a choledochal cyst: A case report

Rojas

Slater

Hicks

et al. 2016

CRCP

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Rhabdomyosarcoma (RMS) involving the biliary tree and choledochal cysts presents with jaundice and abdominal pain. Imaging studies including ultrasound (US), computerized tomography (CT) scan, and magnetic resonance cholangiopancreatography (MRCP) are useful in the diagnosis and evaluation of biliary tree anatomy. We present a patient with biliary RMS initially thought to be a choledochal cyst with intraluminal cystic debris (biliary sludge) that was diagnosed by frozen section examination during cyst resection and subsequently treated with post-operative chemotherapy and radiation.

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Embryonal rhabdomyosarcoma of the ampulla of Vater in early childhood: report of a case and review of literature

Cited by 15 publications

References 12 publications

Differential diagnosis and management of liver tumors in infants

Differential diagnosis and management of liver tumors in infants

Reporte de caso. Rabdomiosarcoma botrioides de la vía biliar

Rhabdomyosarcoma arising within the biliary tract mimicking a choledochal cyst: A case report

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