Rhabdomyosarcoma is a rare soft tissue malignancy derived from myogenic cells. There is very little literature that provides substantial evidence regarding the outcomes of surgical treatment of parameningeal subtype. Endonasal endoscopic resection offers a faster recovery with minimal morbidity, providing a better life quality and immediately adjuvant treatment. Minimally invasive pericranial flap constitute a good alternative in cases with non-viable mucosal vascularized nasoseptal flap. Multimodal treatment ae essential.