Elastolisis dérmica papilar similar a pseudoxantoma elástico

Pitarch, Gerard; Torrijos, Arantxa; García-Melgares, M.L.; Roche, E.; Calatayud, A.; Fortea, José M.

doi:10.1016/s0001-7310(06)73365-8

Cited by 7 publications

(3 citation statements)

References 12 publications

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“…This disease affects more often elderly women and is characterized by asymptomatic and symmetrical yellowish papules localized predominantly on the neck, supraclavicular regions, and flexural areas [2–4]. …”

Section: Discussionmentioning

confidence: 99%

“…The cutaneous lesions are similar in the two pathologies. The main findings of this disease are located in the mid and lower dermis and consist of fragmentation, clumping, and calcification of the elastic fibers [4, 13]. …”

Section: Discussionmentioning

confidence: 99%

“…Clinically the lesions appear as asymptomatic yellow striae-like bands, palpable, disposed horizontally on the lower back, its predominant location. Histologically, these lesions present with an increased number of clumped and fragmented elastic fibers in the mid and deep dermis separated by normal collagen [4, 18]. …”

Section: Discussionmentioning

confidence: 99%

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Pseudoxanthoma Elasticum Papillary Dermal Elastolysis: A Case Report

Alves

Ferreira²,

Vale³

et al. 2010

Dermatology Research and Practice

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PXE-PDE is a rare clinicopathological entity with few cases reported. It affects more often elderly women and is characterized by asymptomatic bilateral and symmetrical yellowish papules localized predominantly on the neck and supraclavicular regions. It is clinically similar to Pseudoxanthoma Elasticum. The authors report a case of a 64-year-old woman presenting asymptomatic, yellowish, non-follicular papules, affecting the occipital and the posterior region of the neck for 1 year. The patient denied pruritic or inflammatory changes, marked solar exposition or trauma on the affected areas. Routine laboratory studies: thoracic x-ray and ophthalmologic examination were normal. The histopathologic examination of a biopsy of one of the cutaneous lesions showed an absence of elastic fibers in the papillary dermis.The diagnosis of Pseudoxanthoma Elasticum—like Papillary Dermal Elastolysis (PXE-PDE) was made. Of great importance is the differential diagnosis with Pseudoxanthoma elasticum (PXE), but we have also to consider other elastolytic disorders: mid-dermal elastolysis (MDE), linear focal elastosis (LFE) and white fibrous papulosis of the neck (WFPN). Until know, there is no effective treatment for this pathology.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%