EHMTI-0310. Headache in children with Sturge-Weber syndrome

Prabhakar, P; Arkush, Leo; Scott, Richard; Aylett, Sarah

doi:10.1186/1129-2377-15-s1-c52

Cited by 2 publications

(1 citation statement)

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“…A study by Prabhakar et al 10 showed that almost 35% of patients experiencing headaches have one more than once a month and 25% describe headache impacting on their daily activities. SWS type 3 is a very rare variant of this neurocutaneous disorder, and the paediatric presentation rarely includes headaches and less likely a ‘Status migrainosus.’ It is very important for physician to differentiate migraine attacks from seizures as both can be presenting features in patients with SWS type 3 and differentiation can sometimes be challenging.…”

Section: Discussionmentioning

confidence: 99%

Sturge-Weber syndrome type 3 manifesting as ‘Status migrainosus’

2016

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Sturge-Weber syndrome (SWS) is a rare neurocutaneous syndrome characterised by facial naevus and leptomeningeal angiomatosis resulting in neurological and ophthalmological complications. In its rare variant, SWS type 3, the clinical hallmark of facial naevus is absent which poses a diagnostic challenge. Here, we present an interesting case of SWS type 3 where a child presented twice with prolonged severe unilateral headache mimicking migraine status followed on both occasions with focal seizures. He developed a dense right-sided homonymous hemianopia, and an urgent brain MRI scan was performed which pointed towards the diagnosis of SWS type 3.

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Section: Discussionmentioning

confidence: 99%