Dyke-Davidoff-Masson syndrome

Behera, Manas Ranjan; Patnaik, Sibabratta; Mohanty, A.R.

doi:10.4103/0976-3147.102646

Cited by 33 publications

(44 citation statements)

References 18 publications

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“…Initially it was thought to be an isolated radiological syndrome, but various clinical manifestations have been described. These include seizures, facial asymmetry, contralateral hemiparesis, mental retardation and sensorineural hearing loss 3. Clinically, such patients can be classified under hemiconvulsion-hemiplegia and epilepsy (HHE) syndrome.…”

Section: Introductionmentioning

confidence: 99%

Dyke-Davidoff-Masson syndrome: a clinicoradiological amalgam

et al. 2014

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Dyke-Davidoff-Masson syndrome is a relatively rare syndrome with its typical clinical and radiological features including facial asymmetry, hemiplegia, cerebral hemiatrophy, mental retardation with calvarial thickening, hypertrophy of sinuses and elevated petrous ridge on imaging. We present here a case of congenital type Dyke-Davidoff-Masson syndrome with some additional features in the form of microcephaly, hypospadias and pachygyria.

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Section: Introductionmentioning

confidence: 99%

Dyke-Davidoff-Masson syndrome: a clinicoradiological amalgam

et al. 2014

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“…Slon, Hershkovitz, and Peled () reported a case of a historical patient that is a 6,000‐year‐old skeleton of an adult male with DDMS. Classically, patients present a varying extent of facial asymmetry or paresis, sensory disturbances, hemiatrophy of body, focal or generalized uncontrolled seizures, contralateral hemiplegia, mental retardation, impaired cognition, learning and speech impairment, and psychiatric problems (Behera, Patnaik, & Mohanty, ; Shrestha, ; Tasdemir, Incesu, Yazicioglu, Belet, & Güngör, ). The syndrome may be either congenital or acquired (e.g., following trauma, infection, or a vascular disorder; Atalar, Icagasioglu, & Tas, ).…”

Section: Discussionmentioning

confidence: 99%

Dyke–Davidoff–Masson syndrome in the Late Bronze and Early Iron Ages Armenia—a cause of trepanation?

Khudaverdyan

Hovhanesyan²,

Engibaryan

et al. 2018

Intl J of Osteoarchaeology

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Intentionally opened skulls are considered to be the most fascinating of palaeopathological findings. This paper regards the discovery of a new trepanated skull dating from the Late Bronze and Early Iron Ages (1500–1400 BC) found at a burial site of Bardzryal, Armenia. Attention was first paid to trepanation technique, second—the description of methods of trepanations, third—to surgical procedures, and finally, to the cause of trepanation. The remains were examined by standard macromorphological and X‐ray methods of bioarchaeology. Bone nodules resulting from Dyke–Davidoff–Masson syndrome (DDMS) were observed on the endocranial surface of the frontal bone of a female. Regardless of provenance DDMS, which seems to be a possible cause of trepanation in women, is rarely seen in historic populations. Along with DDMS, porotic hyperostosis and osteomas were also observed. This observation constituted the first evidence of DDMS in the Late Bronze and Early Iron Age Armenia.

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“…The pathophysiology of DDMS includes cortical hemiatrophy secondary to one-sided cerebral vascular insult, and may be congenital or acquired 1 2. The absence of sulcation in the former differentiates between the two 1.…”

Section: Descriptionmentioning

confidence: 99%

“…Compensatory widening of the diploic space and paranasal sinuses occurs as a consequence. Mimics of DDMS include Sturge-Weber syndrome (which shows the characteristic port wine stain, extensive pial enhancement and dystrophic calcification),2 Rasmusens encephalitis (in which calvarial changes are typically absent)2 and unilateral complete occlusion of the middle cerebral artery (in which the hemiatrophy is in the territory of the middle cerebral artery vascular supply).…”

Section: Descriptionmentioning

confidence: 99%