Duplication of the pinna (polyotia) in a case of Brachmann-de Lange syndrome

Patil, Dilip Pandurang; Iyer, Uma Shridhar; Prasad, Madhva

doi:10.1016/0007-1226(87)90161-5

Cited by 12 publications

(4 citation statements)

References 5 publications

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…If the accessory tragus lesion is large enough, it could resemble polyotia, a congenital external ear defect presenting as an extra auricle . However, this defect is very rare, and to our knowledge there are only five cases reported in the literature …”

Section: Clinical Presentationmentioning

confidence: 96%

See 1 more Smart Citation

Review of accessory tragus with highlights of its associated syndromes

Bahrani¹,

Khachemoune

2014

Int J Dermatology

View full text Add to dashboard Cite

Accessory tragus is a developmental defect involving malformation of part of the external ear. It is a moderately rare congenital condition reported in 1858 by Birkett for the first time. Histological features of accessory tragus include a thin layer of stratum corneum with a rugated epidermis, presence of eccrine glands, and irregular spatial positioning of vellus hair follicles accompanied by sebaceous glands. Accessory tragus is commonly a limited deformity; however, it can be a sign of associated congenital syndromes. It has been shown to be associated with Goldenhar syndrome, Townes-Brocks syndrome, Treacher-Collins syndrome, VACTERL syndrome, and Wolf-Hirschhron syndrome. Surgical excision, the most common form of management of accessory tragus lesions, typically leads to a positive outcome. An extensive search was performed using pubmed.gov, Embase, MedLine, and Googlescholar.com using key words: accessory tragus, congenital malformations of ear, first branchial arch, and embryology. In this paper, we review the clinical and histological presentation, associated syndromes, management, and outcome of accessory tragus.

show abstract

Section: Clinical Presentationmentioning

confidence: 96%

“…7 However, this defect is very rare, and to our knowledge there are only five cases reported in the literature. [20][21][22][23][24] The patient that we report was a 13-year-old male patient with a solitary asymptomatic lesion located in the left preauricular area (Fig. 1).…”

Section: Clinical Presentationmentioning

confidence: 99%

Review of accessory tragus with highlights of its associated syndromes

Bahrani¹,

Khachemoune

2014

Int J Dermatology

View full text Add to dashboard Cite

show abstract

“…Polyotia is an external ear malformation that is characterized by a large accessory ear, and is a clinical entity distinct from a pre-auricular tag [ 1 ]. It is an extremely rare condition; to date, less than 30 cases of polyotia have been reported according to a review of the literature [ 2 3 4 5 6 7 8 9 10 11 12 13 ]. In this report, we present the surgical details and postoperative outcomes of polyotia correction in a 3-year-old girl, along with relevant review of the literature.…”

Section: Introductionmentioning

confidence: 99%

Surgical Treatment of Polyotia

Rha

Kim

2015

Arch Craniofac Surg

View full text Add to dashboard Cite

show abstract

“…Manche der beschriebenen Fälle hatten zusätzliche Fehlbildungen [3 -5, 7]. Dies waren Wangenspalte [3], Lippen-Kiefer-Gaumenspalte [4], ein Brachmann-de Lange-Syndrom [5] oder wie in diesem Fall eine hemifaziale Gesichtsanomalie [7].…”

Section: Introductionunclassified