The annular pancreas (CPJ) is mainly considered in pediatric surgical practice as a pathology of the newborn period, manifested by a picture of duodenal obstruction and having the potential for complete cure. Nevertheless, during the course of life, patients with this defect may develop complications such as chronic pancreatitis, peptic ulcer, pancreatic tumors, changes in the biliary tract, etc., which develop in adulthood and often cause complications and deaths. There are very few descriptions of such complications in children in the available literature, and therefore, we want to provide a clinical case of an 8-year-old boy with a complicated course of CPJ.