Double-outlet right ventricle with restrictive ventricular septal defect

Transcatheter creation and enlargement of ventricular septal defects for relief of ventricular hypertension

“…These and other early case reports form what remains a limited clinical experience with VSD closure in patients with DORV. [4][5][6][7][8][9] We have found that this complication is not unique to patients with DORV and can occur in any patient in whom the native ventricular outflow tract is either congenitally or iatrogenically absent, malpositioned, or severely obstructed, and the VSD constitutes the only means of egress from the nonsystemic ventricle. An unrestrictive atrial communication in these patients averts dramatic clinical presentation but does not obviate the need for intervention.…”