Double orifice mitral valve in a patient with bicuspid aortic valve and coarctation of the aorta: A rare presentation

Bayat, Fariba; Namazi, Mohammad Hasan; Khammarnia, Mohammad; Shekarkhar, Shadi; Fatehi, Aref; Tabary, Mohammadreza; Khaheshi, Isa

doi:10.1002/ccr3.2788

Cited by 2 publications

(2 citation statements)

References 7 publications

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“…There are a few reports on the partial form of Shone's complex presenting with DOMV, BAV, and CoA ( 4 - 9 ). It is well recognized that BAV can coexist with CoA.…”

Section: Discussionmentioning

confidence: 99%

Atypical Shone's Complex Diagnosed at 70 Years Old: Presenting with Double-orifice Mitral Valve, Bicuspid Aortic Valve, and Aortic Coarctation

et al. 2022

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Atypical Shone's complex is a rare congenital anomaly involving a left-sided obstructive lesion of two or three cardiovascular levels. A 70-year-old man with dyspnea on exertion was diagnosed with severe aortic stenosis (AS) with a bicuspid valve, complicated by severe aortic coarctation (CoA) and a double-orifice mitral valve. He underwent surgery for AS and CoA in one session. It is important to search for complicated malformations, even in cases of bicuspid aortic valve found in old age.

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“…There are a few reports on the partial form of Shone's complex presenting with DOMV, BAV, and CoA ( 4 - 9 ). It is well recognized that BAV can coexist with CoA.…”

Section: Discussionmentioning

confidence: 99%

Atypical Shone's Complex Diagnosed at 70 Years Old: Presenting with Double-orifice Mitral Valve, Bicuspid Aortic Valve, and Aortic Coarctation

et al. 2022

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“…A bicuspid aortic valve (BAV) is relatively common and is characterized by the abnormal fusion of two leaflets of the aortic valve (AV) during development, resulting in a two leaflet valve instead of the normal tricuspid AV [ 5 ]. Patients with both DOMV and BAV are rare [ 6 ].…”

Section: Introductionmentioning

confidence: 99%

Rare double orifice mitral valve malformation associated with bicuspid aortic valve in Turner syndrome: diagnosed by a series of novel three-dimensional echocardiography and literature review

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et al. 2021

BMC Cardiovasc Disord

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Background Patients with both double orifice mitral valve (DOMV) and bicuspid aortic valve (BAV) malformation are rare. Although DOMV or BAV can be detected in some genetic syndromes, it has not been reported to simultaneously appear in Turner syndrome (TS). TrueVue, TouchVue, and TrueVue Glass are the latest technologies in advanced three-dimensional echocardiography (3DE), which is an important information supplement to two-dimensional echocardiography (2DE) for the diagnosis of congenital cardiac malformations. Herein we report the novel use of the above-mentioned technologies in the diagnosis and evaluation of a rare, combined valve malformation. Meanwhile, we also reviewed the literature for cases involving both DOMV and BAV and their association with various genetic syndromes. Case presentation We present the case of a 5-year-old girl diagnosed with TS because of a developmental delay. DOMV and BAV were found through echocardiographic examination. Three-dimensional transthoracic echocardiography as well as a series of novel advanced techniques were applied to clearly display the spatial structure of all tiers of the mitral valve apparatus, aortic valve, and arch to facilitate an accurate diagnosis. Conclusions This is the first case in which both DOMV and BAV were associated with TS. Innovative TrueVue and TrueVue Glass offer unprecedented photographic stereoscopic images, while TouchVue technology greatly improved the ultrasonic diagnostic workflow and the diagnostic performance of rare valve malformations by adding virtual light sources to display realistic light-shadow effects.

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Double orifice mitral valve in a patient with bicuspid aortic valve and coarctation of the aorta: A rare presentation

Cited by 2 publications

References 7 publications

Atypical Shone's Complex Diagnosed at 70 Years Old: Presenting with Double-orifice Mitral Valve, Bicuspid Aortic Valve, and Aortic Coarctation

Atypical Shone's Complex Diagnosed at 70 Years Old: Presenting with Double-orifice Mitral Valve, Bicuspid Aortic Valve, and Aortic Coarctation

Rare double orifice mitral valve malformation associated with bicuspid aortic valve in Turner syndrome: diagnosed by a series of novel three-dimensional echocardiography and literature review

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