Double-chambered left ventricle in a young previously healthy man presenting for a routine echocardiographic study (RCD code: IV-1B.2o)

Abstract

A double-chambered left ventricle (DCLV) constitutes a rare congenital malformation. It is usually diagnosed at a neonatal or pediatric age, and often exhibits mixed criteria for diverticulae and aneurysms. This anomaly is characterized by the subdivision of the left ventricle into two chambers by an abnormal septum or muscle band. In this article, we present the case of 30-year-old asymptomatic patient, in whom DCLV was diagnosed by routine echocardiographic study. JRCD 2013; 1 (4): 155-157

The Grave Consequences of Late Presentation and Management of Rare Double Left Ventricle Chamber With Cardiomyopathy

“…A double-chambered left ventricle (DCLV) constitutes an extremely rare congenital malformation, and compared with a double right ventricle (RV), is a more common pathology [1][2][3][4]. A combination of these two in a patient has also been described, although even rarer [5].…”

“…A literature search found that only a few case reports of a DCLV have been described to date in which the left ventricle (LV) anomaly is characterized by the subdivision of the LV into two chambers by an abnormal septum or muscle band [6,7]. The few available reported cases show that cardiomyopathy is often an associated pathology [3,7]. The degree of the clinical symptoms of DCLV is associated with the size of the access hole between the main LV chamber and the accessory chamber and the heart function of the patient [1].…”