Abstract:The Bourneville-Pringle syndrome is an autosomal dominant neurocutaneous disorder
characterized by the development of multiple hamartomas in various systems,
especially brain, skin, retina, kidney, heart and lung. The case of a patient with
brownish plaques on the forehead and temporal region, pink malar and chin papules,
and hypopigmented macules on the back and trunk is described. The diagnosis of the
Bourneville-Pringle syndrome is based on clinical criteria. Presence of two major
criteria, such as facial a… Show more
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