Diagnostic image evaluation of hydranencephaly and pictorially similar entities, with emphasis on computed tomography.

Abstract

The radiographic evaluation of a spectrum of vascular cerebral damage is presented, ranging from simple porencephaly to the most severe form, classic hydranencephaly. With a combination of clinical materal and computed tomography, it is possible in most cases to arrive at a specific diagnosis of hydranencephaly or severe bilateral porencephaly. Pictorially similar entities, such as massive congenital subdural hematomas or hygromas, alobar holoprosencephaly, massive hydrocephalus, and massive postanoxic or infective encephalopathies, are discussed.

Poland anomaly and hydranencephaly: An unusual association

“…Usually leptomeninges and dura remain present. Cerebellum, midbrain, thalami, basal ganglia, choroid plexus, and portions of the occipital lobes are generally preserved, as these receive their vascularization through the posterior circulation, vertebrobasiler system [Dublin and French, 1980; Kurtz and Johnson, 1999]. Stevenson et al [2001] thought that the predominant theory of hydranencephaly was that vascular compromise of the carotid artery system leaded to hydranencephaly and their case had an intrinsic vascular pathway disruption.…”

Hydrocephalus — revision of its definition and classification with special reference to “intractable infantile hydrocephalus”

“…In the treatment of hydrocephalus, it is essential to distinguish severe simple hydrocephalus from non-treatable hydrocephalus. Although severe simple hydrocephalus mimics severe complicated hydrocephalus on CT scan, it is treatable [13,23,701.…”

Delayed Diagnosis of Hydranencephaly in a Nine-Month-Old Child

“…The absent brain is replaced by cerebrospinal fluid (CSF) and the association to hydrocephalus is frequently given. 2,5,6 Diagnosis is usually made intrauterine by ultrasound (US) and/or magnetic resonance imaging (MRI) and leads normally to abortion. 7,8 We present a case of a 9 months old child with delayed diagnosis of hydranencephaly.…”