Diagnosis of arrhythmogenic right ventricular cardiomyopathy by 3 different sets of criteria

Kiès, Philippine; Bootsma, Marianne; Bax, Jeroen J.; Zeppenfeld, Katja; Koning, A.E. De; Vriend, Fleur; Wall, Ernst E. van der; Schalij, Martin J.

doi:10.1016/j.hrthm.2005.02.706

Cited by 2 publications

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“…Because of the patchy myocardial involvement, negative biopsy results do not exclude ARVC. Although previous studies have found histopathological abnormalities in as many as half of all children with ventricular ectopy and structurally normal hearts, 4,15 because of the low yield of this test in our population, the role of endomyocardial biopsy as a diagnostic test in RVOT VT remains unclear. It is important to recognize the diagnostic usefulness of a biopsy in children with myocarditis or cardiomyopathy as a cause of VT in the setting of a structurally normal heart.…”

Section: Discussionmentioning

confidence: 73%

“…11 However, similar subtle MRI abnormalities can be present in RVOT VT. 12,13 Furthermore, in patients being examined for possible ARVC, there is very poor diagnostic concordance among the McKenna, MRI, and ECG criteria. 15 Because of the clinical, radiologic, and electrocardiographic overlap of the 2 conditions, making an early diagnosis is challenging. The prognostic implications of an accurate diagnosis are paramount.…”

Section: Discussionmentioning

confidence: 99%

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Right ventricular outflow tract tachycardia in children

Harris

Potts²,

Fournier³

et al. 2006

The Journal of Pediatrics

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Section: Discussionmentioning

confidence: 73%

Section: Discussionmentioning

confidence: 99%

Right ventricular outflow tract tachycardia in children

Harris

Potts²,

Fournier³

et al. 2006

The Journal of Pediatrics

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Perioperative management of hereditary arrhythmogenic syndromes

Staikou

Chondrogiannis

Mani

2012

British Journal of Anaesthesia

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Patients with inherited cardiac channel disorders are at high risk of perioperative lethal arrhythmias. Preoperative control of symptoms and a multidisciplinary approach are required for a well-planned management. Good haemodynamic monitoring, adequate anaesthesia and analgesia, perioperative maintenance of normocarbia, normothermia, and normovolaemia are important. In congenital long QT syndrome, torsades de pointes should be prevented with magnesium sulphate infusion and avoidance of drugs such as droperidol, succinylcholine, ketamine, and ondansetron. Propofol and epidural anaesthesia represent safe choices, while caution is needed with volatile agents. In Brugada syndrome, β-blockers, α-agonists, and cholinergic drugs should be avoided, while isoproterenol reverses the ECG changes. Propofol, thiopental, and volatiles have been used uneventfully. In congenital sick sinus syndrome, severe bradycardia resistant to atropine may require isoproterenol or epinephrine. Anaesthetics with vagolytic properties are preferable, while propofol and vecuronium should be given with caution due to risk of inducing bradyarrhythmias. Neuraxial anaesthesia should produce the least autonomic imbalance. Arrhythmogenic right ventricular dysplasia/cardiomyopathy induces ventricular tachyarrhythmias, which should be treated with β-blockers. Generally, β-adrenergic stimulation and catecholamine release should be avoided. Halothane and pancuronium are contraindicated, while large doses of local anaesthetics and epinephrine should be avoided in neuraxial blocks. In catecholaminergic polymorphic ventricular tachycardia, β-blocker treatment should be continued perioperatively. Catecholamine release and β-agonists, such as isoproterenol, should be avoided. Propofol and remifentanil are probably safe, while halothane and pancuronium are contraindicated. Regional anaesthesia, without epinephrine, is relatively safe. In suspicious cardiac deaths, postmortem examination and familial screening are recommended.

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Diagnosis of arrhythmogenic right ventricular cardiomyopathy by 3 different sets of criteria

Cited by 2 publications

References 0 publications

Right ventricular outflow tract tachycardia in children

Right ventricular outflow tract tachycardia in children

Perioperative management of hereditary arrhythmogenic syndromes

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