Diagnosis and Surgical Management of Congenital Intranasal Teratoma in a Newborn: A Rare Case Report

Abstract

Teratomas are the most common germ cell tumors of childhood. Head and neck teratomas, however, account for less than five percent of all teratomas. Considered rare at an incidence of 1 in 20,000 to 40,000 live births, they may occur in the cervical region, nasopharynx, brain, orbit, or oropharynx. Teratoma presenting as an isolated intranasal mass is extremely rare. In this report, we describe a case of a mature teratoma arising from the roof of the nasal cavity presenting as an isolated intranasal mass, the first of its kind from our literature review. The tumor was resected endoscopically with no recurrence detected.

Post-auricular teratoma in an HIV-exposed newborn

“… 6 Cleft palate malformation is usually associated with teratoma of the nasopharynx. 7 8 In our case, the infant had a moderate atrial septal defect which did not require immediate intervention. The association of congenital teratoma with HIV exposure needs to be confirmed with further studies.…”

Multidisciplinary approach to children with sinonasal tumors: A review

“…Preoperative magnetic resonance imaging (MRI) and computed tomography (CT) are therefore essential to identify any intracranial extensions or bony skull base defects suggestive of a nasal encephalocoele. This is because treatment is vastly different and would require a multidisciplinary team involving the expertise of a neurosurgeon …”

“…Occurrences have also been described in other regions of the head and neck, such as the brain, orbit, and oropharynx. However, presentation of a teratoma as an isolated intranasal mass is extremely rare …”

“…However, presentation of a teratoma as an isolated intranasal mass is extremely rare. 5 Other benign tumors include encephalocoeles, which are accompanied by other anomalies in most patients. Frontoethmoidal encephalocoeles typically present as nasal broadening or a blue, pulsatile, reducible mass near the nasal bridge that transilluminates.…”

“…neurosurgeon. 5 Cancer of the nasal cavity in children is particularly challenging because of the often nonspecific symptoms and characteristically advanced degree of local destruction at presentation. Tumors of the nasal cavity are often initially misdiagnosed as sinus disease and treated empirically because their symptoms mimic those of other inflammatory nasal diseases.…”