Diagnosis and Innovative Multidisciplinary Management of Hallermann-Streiff Syndrome

Abstract

Hallermann-Streiff syndrome (HSS) is a rare congenital disorder that mainly affects head and face development. We described the different patterns of the disease throughout the whole growth period and provided innovative treatment steps. Indeed, early genioplasty and dental implantation before growth completion were performed. These steps allowed to improve facial growth and to provide orthodontic anchorage, respectively. Complementary orthognathic surgery achieved satisfactory occlusion and refined aesthetics. We believe such an approach could be considered as a relevant treatment modality to complete multidisciplinary care in patients with HSS.

Dental Rehabilitation of a Rare Hallermann-Streiff Syndrome with Olygodontia: A Case Report

“…In this case, the most remarkable dental anomaly was oligodontia characterized by many missing teeth (n≥6). The patient's permanent teeth (except for 16,17,26,27,36,37,46,47,13,23) have been detected missing congenitally by panoramic radiograph. However, it has been suggested that the age of 10 years was critical for confirming the absence of a second premolar (15).…”

“…The incidence of dental anomalies, one of these criteria, was 85% (12). These were mandibular hypoplasia, hypodontia, malocclusion, dental malformation, natal teeth and premature eruption in primary dentition (13). Odontodysplasia (6,14), permanent teeth with the absence of roots, impacted teeth (10), hypoplastic coronoid, and condylar processes (4) were also reported in patients with HSS.…”

“…Therefore, the follow-up of the patient is so important to evaluate the prognosis of tooth agenesis. In a case, a 20year follow-up of the patient with HSS with 16 missing teeth, orthodontic, restorative and prosthetic applications were presented (13). In this case, endodontic and restorative procedures were applied to keep the existing deciduous teeth in the mouth as much as possible.…”

Recent trends in covalent organic frameworks (COFs) for carbon dioxide reduction

“…52 Dong et al reported porous boron-containing covalent organic frameworks, which exhibit strong ion adsorption ability and served as competent additives for Li + ion transference number improvement of the polymer electrolyte. 53 In recent times, Zhang's group prepared and immobilized Boron-based COF onto the surface of a capillary (COF-1@capillary column) and showed its application towards electro chromatographic separation [Fig. 3a].…”

Hallermann-Streiff syndrome: A missing molecular link for a highly recognizable syndrome

“…Maxillary hypoplasia and malocclusion are frequently reported (Parikh & Gupta, ). Dental anomalies are a common finding and may include absence of teeth, premature eruption and persistence of deciduous teeth, missing of multiple permanent teeth, malocclusion and open bite, malformed teeth, severe and premature caries, and especially natal and/or neonatal teeth (Abadi, Van Sickels, McConnell, & Kluemper, ; Dulong et al, ; Hutchinson, ; Sharp & Kopel, ). An optimal oral hygiene is of particular importance for patients with HSS and often they need a multidisciplinary approach to manage the orofacial abnormalities.…”