Desmoplastic Fibroma of the Mandible: Case Report and Review of Literature

Abstract

Desmoplastic fibroma is a rare benign and locally aggressive myofibroblastic tumour, frequently seen in the second or third decades of life. The mandible and the maxilla are infrequently involved, and the mandible is the most commonly affected of the facial bones. Nevertheless, reports of desmoplastic fibroma affecting the mandible are scarce in the literature. This article reports a rare case of desmoplastic fibroma affecting the angle of the mandible in a 10-year-old Indian male. In addition, a review of literature relating to desmoplastic fibroma affecting the angle of the mandible is presented.

Surgical treatment of desmoplastic fibroma in the jaw using mandibular graft reconstruction – a case report

“…Among the surgeons, some prefer curettage, while others defend a wide local excision or resection with margin [10]. Shekhar et al [18] reported recurrence of 20-40% of the cases treated with enucleation or local excision, while those treated only with curettage recurred in 70%. According to Patussi et al [14], the patient underwent four operations in which all were performed in only curettage.…”

“…The treatment proposed was en bloc resection, in order to give enough margin and reduce the possibility of recurrence, according to what is described in the literature. Despite its non-metastatic nature, the aggressiveness of the lesion and the high recurrence rates justify clinical and radiographic follow-up for a long period [18].…”

“…Even though literature suggests trauma and genetic factors as possible causes for expression and development of the lesion, the exact aetiology remains unclear. Clinically, desmoplastic fibroma may present as anasymptomatic swelling that slowly growth [18]. Radiographically, may present different features, regarding the configuration of the lesion (unique or multilocular) and the margins (well or not defined) [12].…”