E ndometriosis is a disease characterized by the presence of uterine tissue outside the endometrium and myometrium (1). It can clinically manifest with dysmenorrhea, dyspareunia, cyclical or noncyclical pelvic pain and subfertility. Occurring in 8% to 15% of menstruating women (2), it most commonly presents in the ovaries, uterine ligaments, rectovaginal septum and peritoneum (3). Endometriosis can less commonly present in other sites such as the intestines, appendix, lungs and kidneys (4). The cutaneous variant of endometriosis is much rarer and has been reported to account for approximately 1% of all cases (5). Cutaneous endometriosis is most prevalent at sites of surgical scars such as those from caesarean sections, episiotomies, hysterectomies, laparoscopies and other abdominal surgeries (2-4,6,7). According to Friedman and Rico (6), umbilical endometriosis with no previous abdominal or pelvic surgery is even less common. Patients with cutaneous endometriosis typically present to the gynecologist and the dermatologist. If they have a history of pelvic or abdominal surgery, then they can also present to the general surgeon. There have been only 81 published reports of 'umbilical endometriosis' in the world between 1953 and 2008. Although patients with umbilical endometriosis infrequently present to the plastic surgeon, we present such a case and suggest that it be kept on the plastic surgeon's differential diagnosis for umbilical lesions.